-
1
-
-
0001752544
-
Cystic fibrosis
-
Scriver C. Sly W. Childs B. Beaudet A. Valle D. Kinzler K. Vogelstein B. editors. New York, NY: McGraw-Hill;
-
Welsh MJ, Ramsey BW, Accurso FJ, Cutting GR, Scriver CR, Beaudet AL,. Cystic fibrosis. In:, Scriver C, Sly W, Childs B, Beaudet A, Valle D, Kinzler K, Vogelstein B, editors. The metabolic and molecular basis of inherited diseases. New York, NY: McGraw-Hill; 2001. pp 5121-5188.
-
(2001)
The Metabolic and Molecular Basis of Inherited Diseases
, pp. 5121-5188
-
-
Welsh, M.J.1
Ramsey, B.W.2
Accurso, F.J.3
Cutting, G.R.4
Scriver, C.R.5
Beaudet, A.L.6
-
2
-
-
34247497283
-
Cystic fibrosis: A review of epidemiology and pathobiology
-
Strausbaugh S, Davis P,. Cystic fibrosis: A review of epidemiology and pathobiology. Clin Chest Med 2007; 28: 279-288.
-
(2007)
Clin Chest Med
, vol.28
, pp. 279-288
-
-
Strausbaugh, S.1
Davis, P.2
-
3
-
-
0036320272
-
Pseudomonas aeruginosa and other predictors of mortality and morbidity in young children with cystic fibrosis
-
Emerson J, Rosenfeld M, McNamara S, Ramsey B, Gibson R,. Pseudomonas aeruginosa and other predictors of mortality and morbidity in young children with cystic fibrosis. Pediatr Pulmonol 2002; 34: 91-100.
-
(2002)
Pediatr Pulmonol
, vol.34
, pp. 91-100
-
-
Emerson, J.1
Rosenfeld, M.2
McNamara, S.3
Ramsey, B.4
Gibson, R.5
-
4
-
-
0142105983
-
Pseudomonas acquisition in young patients with cystic fibrosis: Pathophysiology, diagnosis, and management
-
Rosenfeld M, Ramsey B, Gibson R,. Pseudomonas acquisition in young patients with cystic fibrosis: Pathophysiology, diagnosis, and management. Curr Opin Pulm Med 2003; 9: 492-497.
-
(2003)
Curr Opin Pulm Med
, vol.9
, pp. 492-497
-
-
Rosenfeld, M.1
Ramsey, B.2
Gibson, R.3
-
5
-
-
0035253464
-
Longitudinal assessment of Pseudomonas aeruginosa in young children with cystic fibrosis
-
Burns J, Gibson R, McNamara S, Yim D, Emerson J, Rosenfeld M, et al. Longitudinal assessment of Pseudomonas aeruginosa in young children with cystic fibrosis. J Infect Dis 2001; 183: 444-452.
-
(2001)
J Infect Dis
, vol.183
, pp. 444-452
-
-
Burns, J.1
Gibson, R.2
McNamara, S.3
Yim, D.4
Emerson, J.5
Rosenfeld, M.6
-
6
-
-
33846284918
-
Pseudomonas aeruginosa chronic colonization in cystic fibrosis patients
-
Murray T, Egan M, Kazmierczak B,. Pseudomonas aeruginosa chronic colonization in cystic fibrosis patients. Curr Opin Pediatr 2007; 19: 83-88.
-
(2007)
Curr Opin Pediatr
, vol.19
, pp. 83-88
-
-
Murray, T.1
Egan, M.2
Kazmierczak, B.3
-
7
-
-
12844270608
-
Longitudinal development of mucoid Pseudomonas aeruginosa infection, lung disease progression in children with cystic fibrosis
-
Li Z, Kosorok M, Farrell P, Laxova A, West S, Green C, et al. Longitudinal development of mucoid Pseudomonas aeruginosa infection, lung disease progression in children with cystic fibrosis. JAMA 2005; 293: 581-588.
-
(2005)
JAMA
, vol.293
, pp. 581-588
-
-
Li, Z.1
Kosorok, M.2
Farrell, P.3
Laxova, A.4
West, S.5
Green, C.6
-
8
-
-
0034878704
-
Alginate overproduction affects Pseudomonas aeruginosa biofilm structure and function
-
Hentzer M, Teitzel G, Balzer G, Heydorn A, Molin S, Givskov M, et al. Alginate overproduction affects Pseudomonas aeruginosa biofilm structure and function. J Bacteriol 2001; 183: 5395-5401.
-
(2001)
J Bacteriol
, vol.183
, pp. 5395-5401
-
-
Hentzer, M.1
Teitzel, G.2
Balzer, G.3
Heydorn, A.4
Molin, S.5
Givskov, M.6
-
9
-
-
0026047681
-
Protection of Pseudomonas aeruginosa against ciprofloxacin and beta-lactams by homologous alginate
-
Hodges N, Gordon C,. Protection of Pseudomonas aeruginosa against ciprofloxacin and beta-lactams by homologous alginate. Antimicrob Agents Chemother 1991; 35: 2450-2452.
-
(1991)
Antimicrob Agents Chemother
, vol.35
, pp. 2450-2452
-
-
Hodges, N.1
Gordon, C.2
-
10
-
-
0031661390
-
Long-term follow up of changes in FEV1 and treatment intensity during Pseudomonas aeruginosa colonisation in patients with cystic fibrosis
-
Ballmann M, Rabsch P, von der Hardt H,. Long-term follow up of changes in FEV1 and treatment intensity during Pseudomonas aeruginosa colonisation in patients with cystic fibrosis. Thorax 1998; 53: 732-737.
-
(1998)
Thorax
, vol.53
, pp. 732-737
-
-
Ballmann, M.1
Rabsch, P.2
Von Der Hardt, H.3
-
11
-
-
0032797445
-
Pulmonary outcome in cystic fibrosis is influenced primarily by mucoid Pseudomonas aeruginosa infection and immune status and only modestly by genotype
-
Parad R, Gerard C, Zurakowski D, Nichols D, Pier G,. Pulmonary outcome in cystic fibrosis is influenced primarily by mucoid Pseudomonas aeruginosa infection and immune status and only modestly by genotype. Infect Immun 1999; 67: 4744-4750.
-
(1999)
Infect Immun
, vol.67
, pp. 4744-4750
-
-
Parad, R.1
Gerard, C.2
Zurakowski, D.3
Nichols, D.4
Pier, G.5
-
12
-
-
0026831341
-
Mucoid Pseudomonas aeruginosa is a marker of poor survival in cystic fibrosis
-
Henry R, Mellis C, Petrovic L,. Mucoid Pseudomonas aeruginosa is a marker of poor survival in cystic fibrosis. Pediatr Pulmonol 1992; 12: 158-161.
-
(1992)
Pediatr Pulmonol
, vol.12
, pp. 158-161
-
-
Henry, R.1
Mellis, C.2
Petrovic, L.3
-
13
-
-
34347370866
-
Duration of treatment effect after tobramycin solution for inhalation in young children with cystic fibrosis
-
Gibson R, Emerson J, Mayer-Hamblett N, Burns J, McNamara S, Accurso F, et al. Duration of treatment effect after tobramycin solution for inhalation in young children with cystic fibrosis. Pediatr Pulmonol 2007; 42: 610-623.
-
(2007)
Pediatr Pulmonol
, vol.42
, pp. 610-623
-
-
Gibson, R.1
Emerson, J.2
Mayer-Hamblett, N.3
Burns, J.4
McNamara, S.5
Accurso, F.6
-
14
-
-
59649123905
-
Acquisition,eradication of P. aeruginosa in young children with cystic fibrosis
-
Douglas T, Brennan S, Gard S, Berry L, Gangell C, Stick S, et al. Acquisition,eradication of P. aeruginosa in young children with cystic fibrosis. Eur Respir J 2009; 33: 305-311.
-
(2009)
Eur Respir J
, vol.33
, pp. 305-311
-
-
Douglas, T.1
Brennan, S.2
Gard, S.3
Berry, L.4
Gangell, C.5
Stick, S.6
-
15
-
-
23444434606
-
Early therapy eradication against Pseudomonas aeruginosa in cystic fibrosis patients
-
Taccetti G, Campana S, Festini F, Mascherini M, Döring G,. Early therapy eradication against Pseudomonas aeruginosa in cystic fibrosis patients. Eur Respir J 2005; 26: 458-461.
-
(2005)
Eur Respir J
, vol.26
, pp. 458-461
-
-
Taccetti, G.1
Campana, S.2
Festini, F.3
Mascherini, M.4
Döring, G.5
-
16
-
-
0030995361
-
Antibiotic treatment of initial colonization with Pseudomonas aeruginosa postpones chronic infection and prevents deterioration of pulmonary function in cystic fibrosis
-
Frederiksen B, Koch C, Haiby N,. Antibiotic treatment of initial colonization with Pseudomonas aeruginosa postpones chronic infection and prevents deterioration of pulmonary function in cystic fibrosis. Pediatr Pulmonol 1997; 23: 330-335.
-
(1997)
Pediatr Pulmonol
, vol.23
, pp. 330-335
-
-
Frederiksen, B.1
Koch, C.2
Haiby, N.3
-
17
-
-
55549102981
-
Early aggressive eradication therapy for intermittent Pseudomonas aeruginosa airway colonization in cystic fibrosis patients: 15 years experience
-
Hansen C, Pressler T, Haiby N,. Early aggressive eradication therapy for intermittent Pseudomonas aeruginosa airway colonization in cystic fibrosis patients: 15 years experience. J Cyst Fibros 2008; 7: 523-530.
-
(2008)
J Cyst Fibros
, vol.7
, pp. 523-530
-
-
Hansen, C.1
Pressler, T.2
Haiby, N.3
-
18
-
-
23644439540
-
Eradication of early Pseudomonas aeruginosa infection
-
Haiby N, Frederiksen B, Pressler T,. Eradication of early Pseudomonas aeruginosa infection. J Cyst Fibros 2005; 4: 49-54.
-
(2005)
J Cyst Fibros
, vol.4
, pp. 49-54
-
-
Haiby, N.1
Frederiksen, B.2
Pressler, T.3
-
19
-
-
0033653318
-
Prospects for the prevention and control of pseudomonal infection in children with cystic fibrosis
-
Haiby N,. Prospects for the prevention and control of pseudomonal infection in children with cystic fibrosis. Paediatr Drugs 2000; 2: 451-463.
-
(2000)
Paediatr Drugs
, vol.2
, pp. 451-463
-
-
Haiby, N.1
-
20
-
-
0036708203
-
Early infection and progression of cystic fibrosis lung disease
-
Koch C,. Early infection and progression of cystic fibrosis lung disease. Pediatr Pulmonol 2002; 34: 232-236.
-
(2002)
Pediatr Pulmonol
, vol.34
, pp. 232-236
-
-
Koch, C.1
-
21
-
-
32444449521
-
Anaerobic killing of mucoid Pseudomonas aeruginosa by acidified nitrite derivatives under cystic fibrosis airway conditions
-
Yoon S, Coakley R, Lau G, Lymar S, Gaston B, Karabulut A, et al. Anaerobic killing of mucoid Pseudomonas aeruginosa by acidified nitrite derivatives under cystic fibrosis airway conditions. J Clin Investig 2006; 116: 436-446.
-
(2006)
J Clin Investig
, vol.116
, pp. 436-446
-
-
Yoon, S.1
Coakley, R.2
Lau, G.3
Lymar, S.4
Gaston, B.5
Karabulut, A.6
-
22
-
-
0037445216
-
Significant microbiological effect of inhaled tobramycin in young children with cystic fibrosis
-
Gibson R, Emerson J, McNamara S, Burns J, Rosenfeld M, Yunker A, et al. Significant microbiological effect of inhaled tobramycin in young children with cystic fibrosis. Am J Respir Crit Care Med 2003; 167: 841-849.
-
(2003)
Am J Respir Crit Care Med
, vol.167
, pp. 841-849
-
-
Gibson, R.1
Emerson, J.2
McNamara, S.3
Burns, J.4
Rosenfeld, M.5
Yunker, A.6
-
23
-
-
77953299585
-
Can mucoid Pseudomonas aeruginosa be eradicated in children with cystic fibrosis?
-
McPherson H, Rosenthal M, Bush A,. Can mucoid Pseudomonas aeruginosa be eradicated in children with cystic fibrosis? Pediatr Pulmonol 2010; 45: 566-568.
-
(2010)
Pediatr Pulmonol
, vol.45
, pp. 566-568
-
-
McPherson, H.1
Rosenthal, M.2
Bush, A.3
-
24
-
-
77954649223
-
Quorum sensing,virulence of Pseudomonas aeruginosa during lung infection of cystic fibrosis patients
-
Bjarnsholt T, Jensen PA, Jakobsen TH, Phipps R, Nielsen AK, Rybtke MT, et al. Quorum sensing,virulence of Pseudomonas aeruginosa during lung infection of cystic fibrosis patients. PLoS ONE 2010; 5: e10115.
-
(2010)
PLoS ONE
, vol.5
-
-
Bjarnsholt, T.1
Jensen, P.2
Jakobsen, T.H.3
Phipps, R.4
Nielsen, A.K.5
Rybtke, M.T.6
-
25
-
-
47049115524
-
Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report
-
Farrell P, Rosenstein B, White T, Accurso F, Castellani C, Cutting G, et al. Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report. J Pediatr 2008; 153: S4-S14.
-
(2008)
J Pediatr
, vol.153
-
-
Farrell, P.1
Rosenstein, B.2
White, T.3
Accurso, F.4
Castellani, C.5
Cuttig, G.6
-
26
-
-
0038102859
-
Evaluation of a new definition for chronic Pseudomonas aeruginosa infection in cystic fibrosis patients
-
Lee T, Brownlee K, Conway S, Denton M, Littlewood J,. Evaluation of a new definition for chronic Pseudomonas aeruginosa infection in cystic fibrosis patients. J Cyst Fibros 2003; 2: 29-34.
-
(2003)
J Cyst Fibros
, vol.2
, pp. 29-34
-
-
Lee, T.1
Brownlee, K.2
Conway, S.3
Denton, M.4
Littlewood, J.5
-
27
-
-
84867741934
-
Eradication of mucoid Pseudomonas aeruginosa in patients with cystic fibrosis: A retrospective analysis
-
Troxler R, WHoover W, Britton L, Gerwin A, Rowe S,. Eradication of mucoid Pseudomonas aeruginosa in patients with cystic fibrosis: A retrospective analysis. 23rd Annu North Am Cyst Fibros Conf 2009; 9: S32-S327
-
(2009)
23rd Annu North Am Cyst Fibros Conf
, vol.9
-
-
Troxler, R.1
Whoover, W.2
Britton, L.3
Gerwin, A.4
Rowe, S.5
-
28
-
-
0035002870
-
Clinical outcome after early Pseudomonas aeruginosa infection in cystic fibrosis
-
Nixon G, Armstrong D, Carzino R, Carlin J, Olinsky A, Robertson C, et al. Clinical outcome after early Pseudomonas aeruginosa infection in cystic fibrosis. J Pediatr 2001; 138: 699-704.
-
(2001)
J Pediatr
, vol.138
, pp. 699-704
-
-
Nixon, G.1
Armstrong, D.2
Carzino, R.3
Carlin, J.4
Olinsky, A.5
Robertsn, C.6
-
29
-
-
43249118265
-
Predictors of mucoid Pseudomonas colonization in cystic fibrosis patients
-
Levy H, Kalish L, Cannon C, Garca K, Gerard C, Goldmann D, et al. Predictors of mucoid Pseudomonas colonization in cystic fibrosis patients. Pediatr Pulmonol 2008; 43: 463-471.
-
(2008)
Pediatr Pulmonol
, vol.43
, pp. 463-471
-
-
Levy, H.1
Kalish, L.2
Cannon, C.3
Garca, K.4
Gerard, C.5
Goldman, D.6
-
30
-
-
0034954979
-
Interlobar differences in bronchoalveolar lavage fluid from children with cystic fibrosis
-
Gutierrez J, Grimwood K, Armstrong D, Carlin J, Carzino R, Olinsky A, et al. Interlobar differences in bronchoalveolar lavage fluid from children with cystic fibrosis. Eur Respir J 2001; 17: 281-286.
-
(2001)
Eur Respir J
, vol.17
, pp. 281-286
-
-
Gutierrez, J.1
Grimwood, K.2
Armstrong, D.3
Carlin, J.4
Carzino, R.5
Olinsy, A.6
-
31
-
-
0032718969
-
Diagnostic accuracy of oropharyngeal cultures in infants and young children with cystic fibrosis
-
Rosenfeld M, Emerson J, Accurso F, Armstrong D, Castile R, Grimwood K, et al. Diagnostic accuracy of oropharyngeal cultures in infants and young children with cystic fibrosis. Pediatr Pulmonol 1999; 28: 321-328.
-
(1999)
Pediatr Pulmonol
, vol.28
, pp. 321-328
-
-
Rosenfeld, M.1
Emerson, J.2
Accurso, F.3
Armstrong, D.4
Castile, R.5
Grimwood, K.6
-
32
-
-
84555178426
-
Intrinsic and environmental mutagenesis drive diversification and persistence of Pseudomonas aeruginosa in chronic lung infections
-
Rodriguez-Rojas A, Oliver A, Blazquez J,. Intrinsic and environmental mutagenesis drive diversification and persistence of Pseudomonas aeruginosa in chronic lung infections. J Infect Dis 2012; 205: 121-127.
-
(2012)
J Infect Dis
, vol.205
, pp. 121-127
-
-
Rodriguez-Rojas, A.1
Oliver, A.2
Blazquez, J.3
|