FUS/TLS-immunoreactive neuronal and glial cell inclusions increase with disease duration in familial amyotrophic lateral sclerosis with an R521C FUS/TLS mutation

Journal of Neuropathology and Experimental Neurology

Volumn 71, Issue 9, 2012, Pages 779-788

  Suzuki, Naoki ^a   Kato, Shinsuke ^b   Kato, Masako ^b   Warita, Hitoshi ^a   Mizuno, Hideki ^a   Kato, Masaaki ^a   Shimakura, Naoko ^a   Akiyama, Haruhiko ^c   Kobayashi, Zen ^c   Konno, Hidehiko ^d   Aoki, Masashi ^a  

^a TOHOKU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b TOTTORI UNIVERSITY   (Japan)

^c TOKYO METROPOLITAN INSTITUTE OF MEDICAL SCIENCE   (Japan)

^d National Hospital Organization Sendai Nishitaga Hospital   (Japan)

Author keywords

Autopsy; Basophilic inclusions; Familial amyotrophic lateral sclerosis; Fused in sarcoma translocated in liposarcoma

Indexed keywords

FUSED IN SARCOMA PROTEIN;

ADULT; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; AUTOPSY; BASOPHIL; CELL INCLUSION; CORRELATION ANALYSIS; DISEASE DURATION; FAMILIAL AMYOTROPHIC LATERAL SCLEROSIS; FAMILIAL DISEASE; FEMALE; GENE MUTATION; GLIA CELL; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; MALE; PRIORITY JOURNAL; SPINAL CORD VENTRAL HORN; SUBSTANTIA NIGRA;

ADULT; AMYOTROPHIC LATERAL SCLEROSIS; ARGININE; BRAIN; CYSTEINE; DISEASE PROGRESSION; DNA MUTATIONAL ANALYSIS; DNA-BINDING PROTEINS; FEMALE; HUMANS; INCLUSION BODIES; MALE; MUTATION, MISSENSE; NEUROGLIA; NEURONS; RNA-BINDING PROTEIN FUS; UBIQUITIN;

EID: 84865627046     PISSN: 00223069     EISSN: 15546578     Source Type: Journal    
DOI: 10.1097/NEN.0b013e318264f164     Document Type: Article

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