Familial amyotrophic lateral sclerosis with posterior column degeneration and basophilic inclusion bodies: A clinical, genetic and pathological study

Clinical Neuropathology

Volumn 20, Issue 2, 2001, Pages 53-59

  Tsuchiya, K ^a   Matsunaga, T ^a   Aoki, M ^a   Haga, C ^a   Ooe, K ^a   Abe, K ^a   Ikeda, K ^a   Nakano, I ^a  

^a TOKYO METROPOLITAN MATSUZAWA HOSPITAL   (Japan)

Author keywords

Basophilic inclusion body; Cu Zn superoxide dismutase; Familial amyotrophic lateral sclerosis; Neuropathology

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE;

ADULT; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; BABINSKI REFLEX; BRONCHOPNEUMONIA; CASE REPORT; CELL INCLUSION; CLINICAL FEATURE; DYSARTHRIA; DYSPHAGIA; FAMILIAL DISEASE; FAMILY HISTORY; FEMALE; HUMAN; HYPERREFLEXIA; MUSCLE ATROPHY; MUSCLE WEAKNESS; NERVE CELL DEGENERATION; NEUROPATHOLOGY; PRIORITY JOURNAL; PYRAMIDAL TRACT; SPASTICITY;

ADULT; DNA MUTATIONAL ANALYSIS; FEMALE; FOLLOW-UP STUDIES; HUMANS; INCLUSION BODIES; MIDDLE AGED; MOTOR NEURON DISEASE; NERVE DEGENERATION; NEURONS; PEDIGREE; POSTERIOR HORN CELLS; PYRAMIDAL TRACTS; SPINAL NERVE ROOTS; SPINOCEREBELLAR TRACTS; SUPEROXIDE DISMUTASE;

EID: 0035083369     PISSN: 07225091     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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