Respiratory mechanics in an infant with perinatal lethal hypophosphatasia treated with human recombinant enzyme replacement therapy

Pediatric Pulmonology

Volumn 47, Issue 9, 2012, Pages 917-922

  Rodriguez, Elena ^a   Bober, Michael B ^a   Davey, Lauren ^a   Zamora, Arlene ^a   Li Puma, Annelise B ^a   Chidekel, Aaron ^a   Shaffer, Thomas H ^a,b  

^a NEMOURS ALFRED I DUPONT HOSPITAL FOR CHILDREN   (United States)

^b TEMPLE UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

human recombinant enzyme replacement therapy; hypophosphatasia; noninvasive pulmonary function testing; thoracoabdominal motion analysis; tissue nonspecific alkaline phosphatase

Indexed keywords

ALKALINE PHOSPHATASE; ASFOTASE ALFA; BUDESONIDE; DORNASE ALFA; IPRATROPIUM BROMIDE; PYRIDOXAL 5 PHOSPHATE; SALBUTAMOL;

ADULT RESPIRATORY DISTRESS SYNDROME; ARTICLE; ARTIFICIAL VENTILATION; BREATHING MECHANICS; BRONCHOSCOPY; CASE REPORT; CHEST WALL OSCILLATION; DISSEMINATED INTRAVASCULAR CLOTTING; DRUG WITHDRAWAL; ENDOTRACHEAL INTUBATION; ENZYME REPLACEMENT; HUMAN; HYPOPHOSPHATASIA; INFANT; LUNG COMPLIANCE; LUNG DYSPLASIA; LUNG FUNCTION; LUNG FUNCTION TEST; LUNG RESISTANCE; MALE; MULTIPLE ORGAN FAILURE; NEONATAL RESPIRATORY DISTRESS SYNDROME; PEAK INSPIRATORY FLOW; PERINATAL LETHAL HYPOPHOSPHATASIA; POSITIVE END EXPIRATORY PRESSURE; PREMATURITY; PRIORITY JOURNAL; RESPIRATORY FAILURE; SEPTIC SHOCK; TRACHEOSTOMY; VENTILATOR ASSOCIATED PNEUMONIA;

AIRWAY RESISTANCE; ALKALINE PHOSPHATASE; ENZYME REPLACEMENT THERAPY; HUMANS; HYPOPHOSPHATASIA; IMMUNOGLOBULIN G; INFANT; MALE; RECOMBINANT FUSION PROTEINS; RESPIRATORY FUNCTION TESTS; RESPIRATORY MECHANICS; THORACIC WALL; TIDAL VOLUME;

EID: 84865104399     PISSN: 87556863     EISSN: 10990496     Source Type: Journal    
DOI: 10.1002/ppul.22527     Document Type: Article

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