Febrile infection-related epilepsy syndrome without detectable autoantibodies and response to immunotherapy: A case series and discussion of epileptogenesis in FIRES

Neuropediatrics

Volumn 43, Issue 4, 2012, Pages 209-216

  Van Baalen, Andreas ^a   Häusler, Martin ^b   Plecko Startinig, Barbara ^c   Strautmanis, Jurgis ^d   Vlaho, Stefan ^e   Gebhardt, Boris ^f   Rohr, Axel ^a   Abicht, Angela ^g   Kluger, Gerhard ^h   Stephani, Ulrich ^a   Probst, Christian ⁱ   Vincent, Angela ^j   Bien, Christian G ^k  

^a UNIVERSITY OF KIEL   (Germany)

^b UNIVERSITY HOSPITAL RWTH AACHEN   (Germany)

^c MEDICAL UNIVERSITY OF GRAZ   (Austria)

^d CHILDREN'S CLINICAL UNIVERSITY HOSPITAL   (Latvia)

^e GOETHE UNIVERSITY   (Germany)

^f MVZ Gelnhausen ^*  (Germany)

^g Medical Genetic Centre   (Germany)

^h Epilepsy Center for Children and Adolescents   (Germany)

ⁱ Institute of Experimental Immunology   (Germany)

^j JOHN RADCLIFFE HOSPITAL   (United Kingdom)

^k EPILEPSY CENTER BETHEL   (Germany)

more..

Author keywords

antibody; epilepsy; fires; immunotherapy; infection; inflammation; status epilepticus

Indexed keywords

4 AMINOBUTYRIC ACID B RECEPTOR; AMPA RECEPTOR; ANTIGEN; AUTOANTIBODY; COMPLEMENTARY DNA; DEXAMETHASONE; GLUTAMATE DECARBOXYLASE; GLUTAMATE RECEPTOR; IMMUNOGLOBULIN; METHYLPREDNISOLONE; N METHYL DEXTRO ASPARTIC ACID RECEPTOR; STEROID; VOLTAGE GATED POTASSIUM CHANNEL;

ACUTE DISEASE; ADOLESCENCE; ANTIBODY DETECTION; ANTIBODY RESPONSE; ARTICLE; BRAIN DISEASE; CEREBROSPINAL FLUID; CHILD; CHRONIC DISEASE; CLINICAL ARTICLE; DISEASE COURSE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; EPILEPSY; EPILEPTIC STATE; EPILEPTOGENESIS; FEBRILE INFECTION EPILEPSY RELATED SYNDROME; FEBRILE INFECTION RELATED EPILEPSY SYNDROME; FEMALE; FEVER; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE; IMMUNOHISTOCHEMISTRY; IMMUNOPRECIPITATION; IMMUNOTHERAPY; INCIDENCE; MALE; NERVE CELL; PATHOGENESIS; PHENOTYPE; PLASMAPHERESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; PROSPECTIVE STUDY; RADIOIMMUNOASSAY; RECURRENT DISEASE; SERUM; TISSUE SECTION;

AUTOANTIBODIES; BRAIN; CHILD; CHILD, PRESCHOOL; DIAGNOSIS, DIFFERENTIAL; ENCEPHALITIS; EPILEPSY; FEMALE; HEK293 CELLS; HUMANS; IMMUNOTHERAPY; MAGNETIC RESONANCE IMAGING; MALE; MEMBRANE PROTEINS; NERVE TISSUE PROTEINS; POTASSIUM CHANNELS, VOLTAGE-GATED; PROSPECTIVE STUDIES; PROTEINS; RADIOIMMUNOPRECIPITATION ASSAY; RECEPTORS, AMPA; RECEPTORS, GABA-A; RECEPTORS, N-METHYL-D-ASPARTATE; RETROSPECTIVE STUDIES; TRANSFECTION;

EID: 84865053432     PISSN: 0174304X     EISSN: 14391899     Source Type: Journal    
DOI: 10.1055/s-0032-1323848     Document Type: Article

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