A Newfoundland cohort of familial and sporadic idiopathic pulmonary fibrosis patients: clinical and genetic features

Respiratory Research

Volumn 13, Issue , 2012, Pages

  Fernandez, Bridget A ^a   Fox, George ^a   Bhatia, Rick ^a   Sala, Eric ^a   Noble, Barbara ^a   Denic, Nash ^a   Fernandez, Dzintra ^a   Duguid, Nigel ^a   Dohey, Amanda ^a   Kamel, Fady ^a   Edwards, Laura ^a   Mahoney, Krista ^a   Stuckless, Susan ^a   Parfrey, Patrick S ^a   Woods, Michael O ^a  

^a MEMORIAL UNIVERSITY OF NEWFOUNDLAND   (Canada)

Author keywords

Familial pulmonary fibrosis; Interstitial pneumonia; Surfactant; Telomere; TERT

Indexed keywords

ACETYLCYSTEINE; AZATHIOPRINE; CYCLOPHOSPHAMIDE; DNA; PREDNISONE; PROTEIN; SURFACTANT PROTEIN A2; SURFACTANT PROTEIN C; TELOMERASE; TELOMERASE REVERSE TRANSCRIPTASE; TELOMERASE RNA COMPONENT; UNCLASSIFIED DRUG; SFTPA2 PROTEIN, HUMAN; SFTPC PROTEIN, HUMAN; SURFACTANT PROTEIN A; TERT PROTEIN, HUMAN;

ADULT; AGED; ARTICLE; ASSAY; BONE MARROW HYPOPLASIA; CANADA; CLINICAL FEATURE; COHORT ANALYSIS; FAMILIAL IDIOPATHIC PULMONARY FIBROSIS; FAMILY HISTORY; FEMALE; FIBROSING ALVEOLITIS; GENE MUTATION; GENETIC SCREENING; GENETIC VARIABILITY; HISTOPATHOLOGY; HUMAN; LIVER CIRRHOSIS; LUNG TRANSPLANTATION; MAJOR CLINICAL STUDY; MALE; NUCLEOTIDE SEQUENCE; PHENOTYPE; POPULATION RESEARCH; SPORADIC IDIOPATHIC PULMONARY FIBROSIS; TELOMERE HOMEOSTASIS; BONE MARROW DISEASE; FOUNDER EFFECT; GENETIC ASSOCIATION; GENETICS; MIDDLE AGED; MUTATION; ONSET AGE;

ADULT; AGE OF ONSET; AGED; AGED, 80 AND OVER; BONE MARROW DISEASES; COHORT STUDIES; FEMALE; FOUNDER EFFECT; GENETIC ASSOCIATION STUDIES; HUMANS; IDIOPATHIC PULMONARY FIBROSIS; MALE; MIDDLE AGED; MUTATION; NEWFOUNDLAND AND LABRADOR; PULMONARY SURFACTANT-ASSOCIATED PROTEIN A; PULMONARY SURFACTANT-ASSOCIATED PROTEIN C; TELOMERASE; YOUNG ADULT;

EID: 84864406003     PISSN: 14659921     EISSN: 1465993X     Source Type: Journal    
DOI: 10.1186/1465-9921-13-64     Document Type: Article

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