Genetics in pulmonary fibrosis-familial cases provide clues to the pathogenesis of idiopathic pulmonary fibrosis

American Journal of the Medical Sciences

Volumn 341, Issue 6, 2011, Pages 439-443

  Lawson, William E ^a   Loyd, James E ^a,b   Degryse, Amber L ^a  

^a VANDERBILT UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b VETERANS AFFAIRS MEDICAL CENTER   (United States)

Author keywords

Familial IPF; Genetics; Mutations; Pulmonary fibrosis; Surfactant; Telomerase

Indexed keywords

ELMOD2 PROTEIN; SURFACTANT ASSOCIATED PROTEIN; SURFACTANT PROTEIN A; SURFACTANT PROTEIN A2; SURFACTANT PROTEIN C; TELOMERASE; TELOMERASE REVERSE TRANSCRIPTASE; TELOMERASE RNA COMPONENT; UNCLASSIFIED DRUG;

COHORT ANALYSIS; CONFERENCE PAPER; EXON; FAMILIAL DISEASE; FAMILIAL INTERSTITIAL PNEUMONIA; FIBROSING ALVEOLITIS; GENE EXPRESSION; GENE MUTATION; GENETIC ANALYSIS; GENETIC LINKAGE; HEREDITY; HISTOPATHOLOGY; HUMAN; IMMUNOHISTOCHEMISTRY; INTERSTITIAL LUNG DISEASE; INTERSTITIAL PNEUMONIA; INTRON; LUNG BIOPSY; LUNG FIBROSIS; LUNG TRANSPLANTATION; NONSPECIFIC INTERSTITIAL PNEUMONIA; PATHOGENESIS; PATHOPHYSIOLOGY; SIGNAL TRANSDUCTION; UNFOLDED PROTEIN RESPONSE; USUAL INTERSTITIAL PNEUMONIA;

CYTOSKELETAL PROTEINS; GENETIC LINKAGE; HUMANS; IDIOPATHIC PULMONARY FIBROSIS; MUTATION; PULMONARY FIBROSIS; PULMONARY SURFACTANT-ASSOCIATED PROTEIN A; PULMONARY SURFACTANT-ASSOCIATED PROTEIN C; RNA; TELOMERASE;

EID: 79958178342     PISSN: 00029629     EISSN: 15382990     Source Type: Journal    
DOI: 10.1097/MAJ.0b013e31821a9d7a     Document Type: Conference Paper

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