Sporadic diffuse leucoencephalopathy with axonal spheroids: Report of a profuse and rapid cortical-spinal degeneration

Neurological Sciences

Volumn 33, Issue 4, 2012, Pages 905-909

  Maues De Paula, A ^a   Michel, B ^b   Dickson, D W ^c   Wszolek, Z K ^c   Pellissier, J F ^a  

^a TIMONE HOSPITAL   (France)

^b HÔPITAL SAINTE MARGUERITE   (France)

^c MAYO CLINIC   (United States)

Author keywords

Adult onset leucodystrophy; Adult onset leucoencephalopathy with pigmented glia and spheroids; Diffuse leucoencephalopathy with spheroids; Pigmentary orthochromatic leucodystrophy

Indexed keywords

MYELIN;

ADULT; AMNESIA; ARTICLE; AUTOPSY; BEHAVIOR CHANGE; BRAIN ATROPHY; BRAIN DEGENERATION; CASE REPORT; CELL SWELLING; COGNITIVE DEFECT; COMPUTER ASSISTED TOMOGRAPHY; CORPUS CALLOSUM; DEATH; DEMYELINATION; DIFFUSE LEUKOENCEPHALOPATHY WITH AXONAL SPHEROIDS; FLACCID PARALYSIS; HUMAN; HUMAN TISSUE; LEUKOARAIOSIS; LEUKOENCEPHALOPATHY; MALE; NERVE FIBER DEGENERATION; NUCLEAR MAGNETIC RESONANCE IMAGING; PYRAMIDAL SIGN; PYRAMIDAL TRACT; QUADRIPLEGIA; SINGLE PHOTON EMISSION COMPUTER TOMOGRAPHY; SPHEROID CELL; URINE INCONTINENCE; WHITE MATTER;

ALPHA-SYNUCLEIN; AMYLOID BETA-PROTEIN PRECURSOR; AXONS; CEREBRAL CORTEX; HUMANS; LEUKOENCEPHALOPATHIES; MAGNETIC RESONANCE IMAGING; MALE; MIDDLE AGED; NEUROFILAMENT PROTEINS; SPINAL DISEASES; TAU PROTEINS;

EID: 84863985037     PISSN: 15901874     EISSN: 15903478     Source Type: Journal    
DOI: 10.1007/s10072-011-0817-8     Document Type: Article

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