Adult onset leukodystrophy with neuroaxonal spheroids: Clinical, neuroimaging and neuropathologic observations

Brain Pathology

Volumn 19, Issue 1, 2009, Pages 39-47

  Freeman, Stefanie H ^a   Hyman, Bradley T ^a   Sims, Katherine B ^a   Hedley Whyte, E T ^a   Vossough, Arastoo ^a,b   Frosch, Matthew P ^a   Schmahmann, Jeremy D ^a  

^a MASSACHUSETTS GENERAL HOSPITAL   (United States)

^b HOSPITAL OF THE UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

Hereditary diffuse leukodystrophy; Leukodystrophy; Neuroaxonal spheroids; Pigmented orthochromic leukodystrophy

Indexed keywords

MYELIN;

ADULT; ARTICLE; AUTOPSY; CASE REPORT; COGNITIVE DEFECT; DEMENTIA; DISEASE COURSE; DISEASE SEVERITY; FAMILIAL DISEASE; FEMALE; FRONTAL LOBE; GLIOSIS; HEREDITARY DIFFUSE LEUKOENCEOHALOPATHY WITH SPHEROID; HUMAN; HUMAN TISSUE; LEUKODYSTROPHY; LEUKOENCEPHALOPATHY; MACROPHAGE; MOTOR DYSFUNCTION; NERVE DEGENERATION; NERVE FIBER; NEUROAXONAL SPHEROID; NEUROIMAGING; NEUROPATHOLOGY; NUCLEAR MAGNETIC RESONANCE IMAGING; PIGMENTED ORTHOCHROMATIC LEUKODYSTROPHY; SYMPTOMATOLOGY; WHITE MATTER;

ADULT; AXONS; BRAIN; BRAIN DISEASES; FEMALE; FRONTAL LOBE; HUMANS; LEUKOENCEPHALOPATHY, PROGRESSIVE MULTIFOCAL; MICROSCOPY, ELECTRON; MIDDLE AGED; NEUROAXONAL DYSTROPHIES;

EID: 57449115006     PISSN: 10156305     EISSN: 17503639     Source Type: Journal    
DOI: 10.1111/j.1750-3639.2008.00163.x     Document Type: Article

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