Bilateral orbital Erdheim-Chester disease treated with 12 weekly administrations of VNCOP-B chemotherapy: A case report and a review of literature

Rheumatology International

Volumn 32, Issue 7, 2012, Pages 2209-2213

  Broccoli, Alessandro ^a   Stefoni, Vittorio ^a   Faccioli, Luca ^a   Agostinelli, Claudio ^a   Spinardi, Luca ^a   Trossello, Marco Pastore ^a   Zinzani, Pier Luigi ^a  

^a UNIVERSITY OF BOLOGNA   (Italy)

Author keywords

Chemotherapy; Erdheim Chester disease; Non Langerhans' cells histiocytosis; Orbital involvement; VNCOP B; Xantoma like lesions

Indexed keywords

ALLOPURINOL; BLEOMYCIN; COTRIMOXAZOLE; CYCLOPHOSPHAMIDE; ETOPOSIDE; HYDROXYCHLOROQUINE; METHOTREXATE; MITOXANTRONE; PREDNISONE; STEROID; VINCRISTINE;

ADULT; ALLERGIC ASTHMA; ANTIBIOTIC PROPHYLAXIS; BLOOD CHEMISTRY; CANCER COMBINATION CHEMOTHERAPY; CASE REPORT; CLINICAL FEATURE; COMPUTER ASSISTED TOMOGRAPHY; DRUG EFFICACY; DRUG TOLERABILITY; EDEMA; ERDHEIM CHESTER DISEASE; EYE INJURY; EYELID; FEMALE; HAY FEVER; HISTIOCYTOSIS; HISTOPATHOLOGY; HUMAN; HYPERCHOLESTEROLEMIA; IMMUNOHISTOCHEMISTRY; LOW DRUG DOSE; LYMPHOMA; MEDICAL DOCUMENTATION; MULTIPLE CYCLE TREATMENT; NONHODGKIN LYMPHOMA; NUCLEAR MAGNETIC RESONANCE IMAGING; ORBIT TUMOR; ORBITAL ERDHEIM CHESTER DISEASE; PERIORBITAL EDEMA; PHYSICAL EXAMINATION; PNEUMOCYSTIS PNEUMONIA; PRIORITY JOURNAL; RECTUS FEMORIS MUSCLE; REVIEW; RHEUMATOID ARTHRITIS; SYNOVITIS; SYSTEMIC HISTIOCYTOSIS; TREATMENT DURATION; TREATMENT OUTCOME; TREATMENT RESPONSE; VISUAL DISORDER;

ANTINEOPLASTIC COMBINED CHEMOTHERAPY PROTOCOLS; BLEOMYCIN; CYCLOPHOSPHAMIDE; DRUG ADMINISTRATION SCHEDULE; ERDHEIM-CHESTER DISEASE; ETOPOSIDE; FEMALE; HUMANS; MAGNETIC RESONANCE IMAGING; MIDDLE AGED; MITOXANTRONE; PREDNISONE; TREATMENT OUTCOME; VINCRISTINE;

EID: 84863981382     PISSN: 01728172     EISSN: 1437160X     Source Type: Journal    
DOI: 10.1007/s00296-011-1998-4     Document Type: Review

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