Neurological manifestations and neuroradiological presentation of Erdheim-Chester disease: Report of 6 cases and systematic review of the literature

Journal of Neurology

Volumn 253, Issue 10, 2006, Pages 1267-1277

  Lachenal, Florence ^a   Cotton, François ^a   Desmurs Clavel, Hélène ^b   Haroche, Julien ^c   Taillia, Hervé ^d   Magy, Nadine ^e   Hamidou, Mohamed ^f   Salvatierra, Juan ^g   Piette, Jean Charles ^c   Vital Durand, Denis ^a   Rousset, Hugues ^a  

^a CENTRE HOSPITALIER LYON SUD   (France)

^b EDOUARD HERRIOT HOSPITAL   (France)

^c PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

^d University of Paris Descartes   (France)

^e UNIVERSITY HOSPITAL JEAN MINJOZ   (France)

^f Dept of Internal Medicine ^*  (France)

^g HOSPITAL UNIVERSITARIO VIRGEN DE LAS NIEVES   (Spain)

Author keywords

Brain; Dura mater; Erdheim Chester disease; MRI

Indexed keywords

ALPHA INTERFERON; AZATHIOPRINE; CLADRIBINE; COLCHICINE; CORTICOSTEROID; CYCLOPHOSPHAMIDE; CYCLOSPORIN A; CYTARABINE; DOXORUBICIN; ETOPOSIDE; METHOTREXATE; THALIDOMIDE; VINBLASTINE; VINCRISTINE;

ARTICLE; BRAIN; CEREBELLUM DISEASE; COGNITIVE DEFECT; CRANIAL NERVE PARALYSIS; DEATH; DIABETES INSIPIDUS; DISABILITY; DURA MATER; ERDHEIM CHESTER DISEASE; HEADACHE; HUMAN; MENINGIOMA; MENTAL DISEASE; NEUROLOGIC DISEASE; NEURORADIOLOGY; NUCLEAR MAGNETIC RESONANCE IMAGING; PRIORITY JOURNAL; PYRAMIDAL SIGN; SEIZURE; SENSORY DYSFUNCTION; TUMOR; UNSPECIFIED SIDE EFFECT;

ADULT; DISEASE PROGRESSION; ERDHEIM-CHESTER DISEASE; FEMALE; HUMANS; MAGNETIC RESONANCE IMAGING; MALE; MIDDLE AGED; SEIZURES;

EID: 33750619575     PISSN: 03405354     EISSN: 14321459     Source Type: Journal    
DOI: 10.1007/s00415-006-0160-9     Document Type: Article

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