Ubiquitin-proteasome-rich cytoplasmic structures in neutrophils of patients with Shwachman-Diamond syndrome

Haematologica

Volumn 97, Issue 7, 2012, Pages 1057-1063

  Necchi, Vittorio ^a   Minelli, Antonella ^a   Sommi, Patrizia ^a   Vitali, Agostina ^a   Caruso, Roberta ^b   Longoni, Daniela ^c   Frau, Maria Rita ^d   Nasi, Cristina ^e   De Gregorio, Fabiola ^f   Zecca, Marco ^g   Ricci, Vittorio ^a   Danesino, Cesare ^a   Solcia, Enrico ^a  

^a UNIVERSITY OF PAVIA   (Italy)

^b BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

^c UNIVERSITY OF MILANO BICOCCA   (Italy)

^d Presidio Ospedaliero S Francesco   (Italy)

^e Division of Pediatrics   (Italy)

^f UNIVERSITY OF NAPLES FEDERICO II   (Italy)

^g FONDAZIONE IRCCS POLICLINICO SAN MATTEO   (Italy)

Author keywords

Apoptosis; Autophagy; Particulate cytoplasmic structure; Proteasome; Shwachman Diamond syndrome; Ubiquitin

Indexed keywords

OUTER MEMBRANE PROTEIN; PROTEASOME; PROTEIN P62; UBIQUITIN; UREASE; VACUOLATING TOXIN;

ADOLESCENT; ADULT; APOPTOSIS; ARTICLE; AUTOPHAGY; CHILD; CLINICAL ARTICLE; CONFOCAL MICROSCOPY; CONTROLLED STUDY; GENE; GENE MUTATION; GRANULOCYTE; HUMAN; HUMAN CELL; IMMUNOBLOTTING; IMMUNOCYTOCHEMISTRY; IMMUNOFLUORESCENCE TEST; NEUTROPHIL; PRESCHOOL CHILD; SBDS GENE; SCHOOL CHILD; SHWACHMAN SYNDROME; TRANSMISSION ELECTRON MICROSCOPY;

ADOLESCENT; ADULT; BACTERIAL PROTEINS; BONE MARROW; BONE MARROW DISEASES; CHILD; CHILD, PRESCHOOL; CYTOPLASMIC STRUCTURES; EXOCRINE PANCREATIC INSUFFICIENCY; FEMALE; GENE EXPRESSION; HUMANS; IMMUNOHISTOCHEMISTRY; LIPOMATOSIS; MALE; MICROSCOPY, CONFOCAL; MUTATION; NEUTROPENIA; NEUTROPHILS; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEINS; RNA-BINDING PROTEINS; UBIQUITIN; UBIQUITINATED PROTEINS;

EID: 84863889048     PISSN: 03906078     EISSN: 15928721     Source Type: Journal    
DOI: 10.3324/haematol.2011.048462     Document Type: Article

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