Regional differences in the evolution of lung disease in children with cystic fibrosis

Pediatric Pulmonology

Volumn 47, Issue 7, 2012, Pages 635-640

  Li, Zhanhai ^a   Sanders, Don B ^a   Rock, Michael J ^a   Kosorok, Michael R ^a,b   Collins, Jannette ^c   Green, Christopher G ^a   Brody, Alan S ^c   Farrell, Philip M ^a  

^a UNIVERSITY OF WISCONSIN SCHOOL OF MEDICINE AND PUBLIC HEALTH   (United States)

^b University of North Carolina at Chapel Hill   (United States)

^c UNIVERSITY OF CINCINNATI   (United States)

Author keywords

bronchiectasis; cystic fibrosis; lung disease; mucoid Pseudomonas aeruginosa; upper lobes

Indexed keywords

ADOLESCENT; ARTICLE; BRONCHIECTASIS; CHILD; COMPUTER ASSISTED TOMOGRAPHY; CONTROLLED STUDY; CYSTIC FIBROSIS; DISEASE COURSE; FEMALE; HUMAN; LUNG DISEASE; LUNG NODULE; MAJOR CLINICAL STUDY; MALE; PEDIATRICS; PRESCHOOL CHILD; PRIORITY JOURNAL; SCHOOL CHILD; SCORING SYSTEM; THORAX RADIOGRAPHY;

ADOLESCENT; BRONCHIECTASIS; CHILD; CHILD, PRESCHOOL; CYSTIC FIBROSIS; DISEASE PROGRESSION; FEMALE; HUMANS; LONGITUDINAL STUDIES; LUNG DISEASES; MALE; MASS CHEST X-RAY; SEVERITY OF ILLNESS INDEX; TOMOGRAPHY, X-RAY COMPUTED; WISCONSIN;

EID: 84862162789     PISSN: 87556863     EISSN: 10990496     Source Type: Journal    
DOI: 10.1002/ppul.21604     Document Type: Article

References (20)

1. Ramsey B,. Management of pulmonary disease in patients with cystic fibrosis. N Engl J Med 1996; 335: 179-188.
2. Maffessanti M, Candusso M, Brizzi F, Piovesana F,. Cystic fibrosis in children: HRCT findings and distribution of disease. J Thorac Imaging 1996; 11: 27-38.
3. Santis G, Hodson ME, Strickland B,. High resolution computed tomography in adult cystic fibrosis patients with mild lung disease. Clin Radiol 1991; 44: 20-22.
4. Davis SD, Fordham LA, Brody AS, Noah TL, Retsch-Bogart GZ, Qaqish BF, Yankaskas BC, Johnson RC, Leigh MW,. Computed tomography reflects lower airway inflammation and tracks changes in early cystic fibrosis. Am J Respir Crit Care Med 2007; 175: 943-950.
5. Cleveland R, Neish A, Zurakowski D, Nichols D, Wohl M, Colin A,. Cystic fibrosis: predictors of accelerated decline and distribution of disease in 230 patients. AJR Am J Roentgenol 1998; 171: 1311-1315.
6. Meyer KC, Sharma A,. Regional variability of lung inflammation in cystic fibrosis. Am J Respir Crit Care Med 1997; 156: 1536-1540.
7. Farrell P, Kosorok M, Laxova A, Shen G, Koscik R, Bruns W, Splaingard M, Mischler E,. Nutritional benefits of neonatal screening for cystic fibrosis. Wisconsin Cystic Fibrosis Neonatal Screening Study Group. N Engl J Med 1997; 337: 963-969.
8. Farrell PM,. Improving the health of patients with cystic fibrosis through newborn screening. Wisconsin Cystic Fibrosis Neonatal Screening Study Group. Adv Pediatr 2000; 47: 79-115.
9. Koscik R, Kosorok M, Farrell P, Collins J, Peters M, Laxova A, Green C, Zeng L, Rusakow L, Hardie R, et al. Wisconsin cystic fibrosis chest radiograph scoring system: validation and standardization for application to longitudinal studies. Pediatr Pulmonol 2000; 29: 457-467.
10. Weatherly M, Palmer C, Peters M, Green C, Fryback D, Langhough R, Farrell P,. Wisconsin cystic fibrosis chest radiograph scoring system. Pediatrics 1993; 91: 488-495.
11. Farrell P, Kosorok M, Rock M, Laxova A, Zeng L, Lai H, Hoffman G, Laessig R, Splaingard M,. Early diagnosis of cystic fibrosis through neonatal screening prevents severe malnutrition and improves long-term growth. Wisconsin Cystic Fibrosis Neonatal Screening Study Group. Pediatrics 2001; 107: 1-13.
12. Button BM, Heine RG, Catto-Smith AG, Olinsky A, Phelan PD, Ditchfield MR, Story I,. Chest physiotherapy in infants with cystic fibrosis: to tip or not? A five-year study. Pediatr Pulmonol 2003; 35: 208-213.
13. Farrell P, Collins J, Broderick L, Rock M, Li Z, Kosorok M, Laxova A, Gershan W, Brody A,. Association between mucoid Pseudomonas infection and bronchiectasis in children with cystic fibrosis. Radiology 2009; 252: 534-543.
14. Li Z, Kosorok M, Farrell P, Laxova A, West S, Green C, Collins J, Rock M, Splaingard M,. Longitudinal development of mucoid Pseudomonas aeruginosa infection and lung disease progression in children with cystic fibrosis. JAMA 2005; 293: 581-588.
15. Tomashefski JF, Bruce M, Goldberg HI, Dearborn DG,. Regional distribution of macroscopic lung disease in cystic fibrosis. Am Rev Respir Dis 1986; 133: 535-540.
16. Khan TZ, Wagener JS, Bost T, Martinez J, Accurso FJ, Riches DW,. Early pulmonary inflammation in infants with cystic fibrosis. Am J Respir Crit Care Med 1995; 151: 1075-1082.
17. Stick SM, Brennan S, Murray C, Douglas T, von Ungern-Sternberg BS, Garratt LW, Gangell CL, De Klerk N, Linnane B, Ranganathan S, et al. Bronchiectasis in infants and preschool children diagnosed with cystic fibrosis after newborn screening. J Pediatr 2009; 155: 623.e1-628.e1.
18. Stafler P, Davies JC, Balfour-Lynn IM, Rosenthal M, Bush A,. Bronchoscopy in cystic fibrosis infants diagnosed by newborn screening. Pediatr Pulmonol 2011; 46: 696-700.
19. Borowitz D, Robinson KA, Rosenfeld M, Davis SD, Sabadosa KA, Spear SL, Michel SH, Parad RB, White TB, Farrell PM, et al. Cystic Fibrosis Foundation evidence-based guidelines for management of infants with cystic fibrosis. J Pediatr 2009; 155: S73-S93.
20. Rosenfeld M, Emerson J, Accurso F, Armstrong D, Castile R, Grimwood K, Hiatt P, McCoy K, McNamara S, Ramsey B, et al. Diagnostic accuracy of oropharyngeal cultures in infants and young children with cystic fibrosis. Pediatr Pulmonol 1999; 28: 321-328.