Myelinating and demyelinating phenotype of Trembler-J mouse (a model of Charcot-Marie-Tooth human disease) analyzed by atomic force microscopy and confocal microscopy

Journal of Molecular Recognition

Volumn 25, Issue 5, 2012, Pages 247-255

  Rosso, Gonzalo ^a   Negreira, Carlos ^c   Sotelo, José R ^a   Kun, Alejandra ^a,b  

^a INSTITUTO DE INVESTIGACIONES BIOLÓGICAS CLEMENTE ESTABLE   (Uruguay)

^b UNIVERSIDAD DE LA REPÚBLICA   (Uruguay)

^c INSTITUTO DE FÍSICA   (Uruguay)

Author keywords

atomic force microscopy; mechanical properties; nerve topography; PMP 22; Trembler J mouse

Indexed keywords

ACTIN; COLLAGEN TYPE 4; MYELIN PROTEIN; PMP22 PROTEIN, MOUSE;

ANIMAL; ATOMIC FORCE MICROSCOPY; C57BL MOUSE; CONFERENCE PAPER; CONFOCAL MICROSCOPY; DISEASE MODEL; ENZYME IMMUNOASSAY; FEMALE; HEREDITARY MOTOR SENSORY NEUROPATHY; HUMAN; METABOLISM; MOUSE; MOUSE MUTANT; MYELIN SHEATH; PATHOLOGY; PERIPHERAL NERVE; SCHWANN CELL; ULTRASTRUCTURE;

ACTINS; ANIMALS; CHARCOT-MARIE-TOOTH DISEASE; COLLAGEN TYPE IV; DISEASE MODELS, ANIMAL; FEMALE; HUMANS; IMMUNOENZYME TECHNIQUES; MICE; MICE, INBRED C57BL; MICE, NEUROLOGIC MUTANTS; MICROSCOPY, ATOMIC FORCE; MICROSCOPY, CONFOCAL; MYELIN PROTEINS; MYELIN SHEATH; PERIPHERAL NERVES; SCHWANN CELLS;

ANIMALIA;

EID: 84860368173     PISSN: 09523499     EISSN: 10991352     Source Type: Journal    
DOI: 10.1002/jmr.2176     Document Type: Conference Paper

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