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Volumn 67, Issue 5, 2012, Pages 382-384

Hot off the breath: 'I've a cost for' - The 64 million dollar question

Author keywords

[No Author keywords available]

Indexed keywords

ASPARTIC ACID; GLYCINE; IVACAFTOR; LUMACAFTOR;

EID: 84859846041     PISSN: 00406376     EISSN: 14683296     Source Type: Journal    
DOI: 10.1136/thoraxjnl-2012-201798     Document Type: Editorial
Times cited : (26)

References (14)
  • 1
    • 33847711906 scopus 로고    scopus 로고
    • Cystic fibrosis mortality and survival in the UK: 1947-2003
    • DOI 10.1183/09031936.00099506
    • Dodge JA, Lewis PA, Stanton M, et al. Cystic fibrosis mortality and survival in the UK: 1947-2003. Eur Respir J 2007;29:522-6. (Pubitemid 46372100)
    • (2007) European Respiratory Journal , vol.29 , Issue.3 , pp. 522-526
    • Dodge, J.A.1    Lewis, P.A.2    Stanton, M.3    Wilsher, J.4
  • 2
    • 78549279173 scopus 로고    scopus 로고
    • Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation
    • Accurso FJ, Rowe SM, Clancy JP, et al. Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation. N Engl J Med 2010;363: 1991-2003.
    • (2010) N Engl J Med , vol.363 , pp. 1991-2003
    • Accurso, F.J.1    Rowe, S.M.2    Clancy, J.P.3
  • 5
    • 0037190575 scopus 로고    scopus 로고
    • Long term azithromycin in children with cystic fibrosis: A randomised, placebo-controlled crossover trial
    • DOI 10.1016/S0140-6736(02)11081-6
    • Equi A, Balfour-Lynn IM, Bush A, et al. Long term azithromycin in children with cystic fibrosis: a randomized, placebo-controlled crossover trial. Lancet 2002;360:978-84. (Pubitemid 35284109)
    • (2002) Lancet , vol.360 , Issue.9338 , pp. 978-984
    • Equi, A.1    Balfour-Lynn, I.M.2    Bush, A.3    Rosenthal, M.4
  • 6
    • 77951887288 scopus 로고    scopus 로고
    • Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa: A randomized controlled trial
    • AZ0004 Azithromycin Study Group
    • Saiman L, Anstead M, Mayer-Hamblett N, et al; AZ0004 Azithromycin Study Group. Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa: a randomized controlled trial. JAMA 2010;303:1707-15.
    • (2010) JAMA , vol.303 , pp. 1707-1715
    • Saiman, L.1    Anstead, M.2    Mayer-Hamblett, N.3
  • 7
    • 0019809960 scopus 로고
    • Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis
    • Knowles M, Gatzy J, Boucher R. Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis. N Engl J Med 1981;305:1489-95. (Pubitemid 12244203)
    • (1981) New England Journal of Medicine , vol.305 , Issue.25 , pp. 1489-1495
    • Knowles, M.1    Gatzy, J.2    Boucher, R.3
  • 8
    • 2442718786 scopus 로고    scopus 로고
    • + absorption produces cystic fibrosis-like lung disease in mice
    • DOI 10.1038/nm1028
    • Mall M, Grubb BR, Harkema JR, et al. Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice. Nat Med 2004;10:487-93. (Pubitemid 38667907)
    • (2004) Nature Medicine , vol.10 , Issue.5 , pp. 487-493
    • Mall, M.1    Grubb, B.R.2    Harkema, J.R.3    O'Neal, W.K.4    Boucher, R.C.5
  • 9
  • 10
    • 52049108262 scopus 로고    scopus 로고
    • Management of asthma based on exhaled nitric oxide in addition to guideline-based treatment for inner-city adolescents and young adults: A randomised controlled trial
    • Szefler SJ, Mitchell H, Sorkness CA, et al. Management of asthma based on exhaled nitric oxide in addition to guideline-based treatment for inner-city adolescents and young adults: a randomised controlled trial. Lancet 2008;372:1065-72.
    • (2008) Lancet , vol.372 , pp. 1065-1072
    • Szefler, S.J.1    Mitchell, H.2    Sorkness, C.A.3
  • 11
    • 77956366627 scopus 로고    scopus 로고
    • Management of severe asthma in children
    • Bush A, Saglani S. Management of severe asthma in children. Lancet 2010;376:814-25.
    • (2010) Lancet , vol.376 , pp. 814-825
    • Bush, A.1    Saglani, S.2
  • 12
    • 84859814270 scopus 로고    scopus 로고
    • Up the cystic fibrosis pulmonary creek in a barbed wire canoe
    • Bush A. Up the cystic fibrosis pulmonary creek in a barbed wire canoe. Pediatr Pulmonol 2011;(Supp 34):118-19.
    • (2011) Pediatr Pulmonol , Issue.SUPPL. 34 , pp. 118-119
    • Bush, A.1
  • 14
    • 84855202429 scopus 로고    scopus 로고
    • Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation
    • Clancy JP, Rowe SM, Accurso FJ, et al. Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation. Thorax 2012;67:12-18.
    • (2012) Thorax , vol.67 , pp. 12-18
    • Clancy, J.P.1    Rowe, S.M.2    Accurso, F.J.3


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.