Microscale oxygraphy reveals OXPHOS impairment in MRC mutant cells

Mitochondrion

Volumn 12, Issue 2, 2012, Pages 328-335

  Invernizzi, F ^a   D'Amato, I ^a   Jensen, P B ^b   Ravaglia, S ^c   Zeviani, M ^a   Tiranti, V ^a  

^a DEPARTMENT OF NEUROSURGERY   (Italy)

^b SeaHorse Bioscience Europe   (Denmark)

^c UNIVERSITY OF PAVIA   (Italy)

Author keywords

Micro oxygraphy; Mitochondrial disorders; OXPHOS; Spectrophotometry

Indexed keywords

ADENOSINE TRIPHOSPHATE;

ACIDIFICATION; ARTICLE; CELL MUTANT; COMPARATIVE EFFECTIVENESS; CONTROLLED STUDY; DIAGNOSTIC TEST ACCURACY STUDY; DISEASE ASSOCIATION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FIBROBLAST; HIGH THROUGHPUT SCREENING; HUMAN; HUMAN CELL; INSTRUMENT VALIDATION; INTERMETHOD COMPARISON; MEASUREMENT; MICROSCALE OXYGRAPHY; MITOCHONDRIAL RESPIRATION; MUTATIONAL ANALYSIS; OXIDATIVE PHOSPHORYLATION; OXIDATIVE PHOSPHORYLATION UNCOUPLING; OXYGEN CONSUMPTION; PRIORITY JOURNAL; RESPIRATORY CHAIN; SENSITIVITY AND SPECIFICITY; SPECTROPHOTOMETRY; TISSUE SPECIFICITY;

CLINICAL LABORATORY TECHNIQUES; HUMANS; MITOCHONDRIA; MITOCHONDRIAL DISEASES; OXIDATIVE PHOSPHORYLATION; SENSITIVITY AND SPECIFICITY; TIME FACTORS;

EID: 84858004724     PISSN: 15677249     EISSN: 18728278     Source Type: Journal    
DOI: 10.1016/j.mito.2012.01.001     Document Type: Article

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