Telomere length is associated with disease severity and declines with age in dyskeratosis congenita

Haematologica

Volumn 97, Issue 3, 2012, Pages 353-359

  Alter, Blanche P ^a   Rosenberg, Philip S ^a   Giri, Neelam ^a   Baerlocher, Gabriela M ^b   Lansdorp, Peter M ^c   Savage, Sharon A ^a  

^a NATIONAL CANCER INSTITUTE   (United States)

^b UNIVERSITY OF BERN   (Switzerland)

^c BRITISH COLUMBIA CANCER AGENCY   (Canada)

Author keywords

Bone marrow failure; Dyskeratosis congenita; Longitudinal study; Telomeres

Indexed keywords

ADULT; AGE; AGED; ARTICLE; CHILD; COHORT ANALYSIS; CONTROLLED STUDY; CROSS-SECTIONAL STUDY; DENDRITIC CELL; DISEASE ASSOCIATION; DISEASE SEVERITY; DKC1 GENE; DYSKERATOSIS CONGENITA; FEMALE; FLUORESCENCE IN SITU HYBRIDIZATION; GENE MUTATION; GENE PRODUCT; GENETIC DISORDER; GENETIC VARIABILITY; GRANULOCYTE; HOYERAAL HREIDARSSON SYNDROME; HUMAN; HUMAN CELL; INFANT; LEUKOCYTE; LONGITUDINAL STUDY; LYMPHOCYTE; LYMPHOCYTE SUBPOPULATION; MAJOR CLINICAL STUDY; MALE; PREDICTIVE VALUE; PRESCHOOL CHILD; REVESZ SYNDROME; SCHOOL CHILD; SENSITIVITY AND SPECIFICITY; TELOMERE HOMEOSTASIS; TINF2 GENE;

ADOLESCENT; ADULT; AGE FACTORS; AGED; AGING; CHILD; CHILD, PRESCHOOL; DISEASE PROGRESSION; DYSKERATOSIS CONGENITA; FEMALE; HUMANS; INFANT; INFANT, NEWBORN; LONGITUDINAL STUDIES; MALE; MIDDLE AGED; TELOMERE SHORTENING; YOUNG ADULT;

EID: 84857769403     PISSN: 03906078     EISSN: 15928721     Source Type: Journal    
DOI: 10.3324/haematol.2011.055269     Document Type: Article

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