Folding delay and structural perturbations caused by type IV collagen natural interruptions and nearby Gly missense mutations

Journal of Biological Chemistry

Volumn 287, Issue 6, 2012, Pages 4368-4375

  Hwang, Eileen S ^a   Brodsky, Barbara ^a,b  

^a RUTGERS ROBERT WOOD JOHNSON MEDICAL SCHOOL   (United States)

^b Tufts University   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID SEQUENCE; BASEMENT MEMBRANE; COLLAGEN TRIPLE HELIX; GENETIC DISEASE; HIGH THERMAL STABILITY; PATHOLOGICAL MUTATIONS; PROTEASE DIGESTION; STRUCTURAL PERTURBATION; THERMOLYSIN; TRIPLE HELIXES;

AMINO ACIDS;

COLLAGEN;

COLLAGEN TYPE 4; GLYCINE; PROTEINASE; SERINE; THERMOLYSIN; TRYPSIN;

AMINO ACID SEQUENCE; ARTICLE; COLLAGEN DISEASE; CONTROLLED STUDY; ENZYME DEGRADATION; MELTING POINT; MISSENSE MUTATION; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN CONFORMATION; PROTEIN FOLDING; PROTEIN STRUCTURE; THERMOSTABILITY; TRIPLE HELIX;

AMINO ACID SUBSTITUTION; COLLAGEN DISEASES; COLLAGEN TYPE IV; GLYCINE; HUMANS; MUTATION, MISSENSE; PROTEIN FOLDING; PROTEIN STRUCTURE, SECONDARY;

BACTERIA (MICROORGANISMS);

EID: 84856713125     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M111.269084     Document Type: Article

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