Structural and biochemical insight into glycogenin inactivation by the glycogenosis-causing T82M mutation

FEBS Letters

Volumn 586, Issue 3, 2012, Pages 254-257

  Carrizo, María E ^a   Romero, Jorge M ^a   Issoglio, Federico M ^a   Curtino, Juan A ^a  

^a Centro de Investigaciones En Quimica Biologica de Cordoba   (Argentina)

Author keywords

Autoglucosylation; Crystal structure; Glycogenin; Glycogenosis; Transglucosylation; UDP glucose hydrolysis

Indexed keywords

ASPARTIC ACID; GLYCOGEN; GLYCOGENIN; HYDROGEN; METHIONINE; SERINE; THREONINE; TYROSINE; URIDINE DIPHOSPHATE GLUCOSE; VALINE;

AMINO ACID SUBSTITUTION; ARTICLE; BINDING AFFINITY; BIOCHEMISTRY; CARBOHYDRATE SYNTHESIS; GENE MUTATION; GLUCOSE TRANSPORT; GLYCOGENOLYSIS; GLYCOSYLATION; HYDROGEN BOND; HYDROLYSIS; NONHUMAN; PRIORITY JOURNAL; PROTEIN INTERACTION; PROTEIN STRUCTURE; RABBIT; X RAY CRYSTALLOGRAPHY;

AMINO ACID SUBSTITUTION; ANIMALS; APOENZYMES; CRYSTALLOGRAPHY, X-RAY; ENZYME ACTIVATION; GLUCOSIDES; GLUCOSYLTRANSFERASES; GLYCOGEN STORAGE DISEASE; GLYCOPROTEINS; GLYCOSYLATION; HYDROGEN BONDING; HYDROLYSIS; MODELS, MOLECULAR; MUSCLES; MUTANT PROTEINS; MUTATION; PROTEIN CONFORMATION; RABBITS; URIDINE DIPHOSPHATE GLUCOSE;

ORYCTOLAGUS CUNICULUS;

EID: 84856222622     PISSN: 00145793     EISSN: 18733468     Source Type: Journal    
DOI: 10.1016/j.febslet.2011.12.028     Document Type: Article

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