Disruption of cytokeratin-8 interaction with F508del-CFTR corrects its functional defect

Human Molecular Genetics

Volumn 21, Issue 3, 2012, Pages 623-634

  Colas, Julien ^a   Faure, Grazyna ^b   Saussereau, Emilie ^a   Trudel, Stéphanie ^a   Rabeh, Wael M ^c   Bitam, Sara ^a   Guerrera, Ida Chiara ^a   Fritsch, Janine ^a   Sermet gaudelus, Isabelle ^a   Davezac, Noëlie ^a,e   Brouillard, Franck ^a   Lukacs, Gergely L ^c   Herrmann, Harald ^d   Ollero, Mario ^a,f   Edelman, Aleksander ^a  

^a UNIVERSITÉ PARIS DESCARTES   (France)

^b CNRS   (France)

^c MCGILL UNIVERSITY   (Canada)

^d GERMAN CANCER RESEARCH CENTER DKFZ   (Germany)

^e UNIVERSITÉ PAUL SABATIER   (France)

^f UNIVERSITÉ PARIS EST CRÉTEIL   (France)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOKERATIN 18; CYTOKERATIN 8; IODIDE; NUCLEOTIDE BINDING DOMAIN 1; NUCLEOTIDE BINDING PROTEIN; SMALL INTERFERING RNA; TRANSMEMBRANE CONDUCTANCE REGULATOR; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ARTICLE; CELL CULTURE; CONTROLLED STUDY; CYSTIC FIBROSIS; DELETION MUTANT; EFFUSION; EPITHELIUM CELL; FEMALE; GEL ELECTROPHORESIS; GENETIC TRANSFECTION; HELA CELL; HUMAN; HUMAN CELL; IMMUNOPRECIPITATION; IN VIVO STUDY; LIGATION; MALE; MASS SPECTROMETRY; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN EXPRESSION; PROTEIN PROTEIN INTERACTION; RESPIRATORY SYSTEM; SURFACE PLASMON RESONANCE;

ANIMALS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EPITHELIAL CELLS; FEMALE; GENE SILENCING; HELA CELLS; HUMANS; KERATIN-18; KERATIN-8; MALE; MICE; MUTATION; NOSE; PROTEIN INTERACTION DOMAINS AND MOTIFS;

MUS;

EID: 84856096159     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddr496     Document Type: Article

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