Congenital hepatic fibrosis and portal hypertension in autosomal dominant polycystic kidney disease

Journal of Pediatric Gastroenterology and Nutrition

Volumn 54, Issue 1, 2012, Pages 83-89

  O'Brien, Kevin ^a   Font Montgomery, Esperanza ^a   Lukose, Linda ^a   Bryant, Joy ^a   Piwnica Worms, Katie ^a   Edwards, Hailey ^a   Riney, Lauren ^a   Garcia, Angelica ^a   Daryanani, Kailash ^b   Choyke, Peter ^c   Mohan, Parvathi ^d   Heller, Theo ^e   Gahl, William A ^a   Gunay Aygun, Meral ^a  

^a NATIONAL HUMAN GENOME RESEARCH INSTITUTE   (United States)

^b National Institutes   (United States)

^c NATIONAL CANCER INSTITUTE   (United States)

^d CHILDREN'S NATIONAL MEDICAL CENTER   (United States)

^e NATIONAL INSTITUTE OF DIABETES AND DIGESTIVE AND KIDNEY DISEASES   (United States)

Author keywords

autosomal dominant polycystic kidney disease; autosomal recessive polycystic kidney disease; congenital hepatic fibrosis; polycystic liver disease; portal hypertension

Indexed keywords

FIBROCYSTIN; LIVER ENZYME; POLYCYSTIN 1;

ADOLESCENT; ADULT; ARTICLE; AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE; CHEMICAL ANALYSIS; CHILD; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED CLINICAL TRIAL; CONTROLLED STUDY; ECHOGRAPHY; ENZYME BLOOD LEVEL; FEMALE; GENE MUTATION; GENE SEQUENCE; GENETIC DISORDER; GENETIC VARIABILITY; HUMAN; IMAGING SYSTEM; KIDNEY POLYCYSTIC DISEASE; LEUKOPENIA; LIVER FIBROSIS; LIVER FUNCTION TEST; MALE; MODIFIER GENE; NUCLEAR MAGNETIC RESONANCE IMAGING; PATHOGENESIS; PORTAL HYPERTENSION; PRESCHOOL CHILD; PRIORITY JOURNAL; SCHOOL CHILD; THROMBOCYTOPENIA;

ADOLESCENT; ADULT; AGED; CHILD; CHILD, PRESCHOOL; CHROMOSOMES; FEMALE; GENES, MODIFIER; HUMANS; HYPERTENSION, PORTAL; LIVER; LIVER CIRRHOSIS; MALE; MIDDLE AGED; MUTATION; POLYCYSTIC KIDNEY, AUTOSOMAL DOMINANT; RECEPTORS, CELL SURFACE; TRPP CATION CHANNELS; YOUNG ADULT;

EID: 84855344038     PISSN: 02772116     EISSN: 15364801     Source Type: Journal    
DOI: 10.1097/MPG.0b013e318228330c     Document Type: Article

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