Alkyl-glycerol rescues plasmalogen levels and pathology of ether-phospholipid deficient mice

PLoS ONE

Volumn 6, Issue 12, 2011, Pages

  Brites, Pedro ^a,b   Ferreira, Ana Sofia ^b   da Silva, Tiago Ferreira ^a,c   Sousa, Vera F ^a,c   Malheiro, Ana R ^a   Duran, Marinus ^b   Waterham, Hans R ^b   Baes, Myriam ^d   Wanders, Ronald J A ^b  

^a UNIVERSITY OF PORTO   (Portugal)

^b UNIVERSITY OF AMSTERDAM   (Netherlands)

^c UNIVERSITY OF PORTO   (Portugal)

^d DEPARTMENT OF PHARMACEUTICAL AND PHARMACOLOGICAL SCIENCES   (Belgium)

Author keywords

[No Author keywords available]

Indexed keywords

1 O OCTADECYLRAC GLYCEROL; AGENTS AFFECTING LIPID METABOLISM; ETHER PHOSPHOLIPID; FAT DROPLET; PLASMALOGEN; UNCLASSIFIED DRUG; CELL RECEPTOR; GLYCEROL; LIPID; PEROXISOMAL TARGETING SIGNAL 2 RECEPTOR; PHOSPHOLIPID;

ADIPOSE TISSUE; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CHONDRODYSPLASIA PUNCTATA; CONTROLLED STUDY; DISORDERS OF LIPID AND LIPOPROTEIN METABOLISM; DRUG EFFICACY; DRUG MECHANISM; ETHER PHOSPHOLIPID DEFICIENCY; FOOD COMPOSITION; FOOD INTAKE; HARDER GLAND; HISTOPATHOLOGY; IN VIVO STUDY; LIPID BLOOD LEVEL; LIPOGENESIS; MOUSE; NERVE CONDUCTION; NERVOUS TISSUE; NONHUMAN; TARGET ORGAN; TESTIS DISEASE; TISSUE DISTRIBUTION; TISSUE LEVEL; WILD TYPE; ANIMAL; ANIMAL FOOD; CELL LINE; CHEMISTRY; ELECTROPHYSIOLOGY; GENETICS; GENOTYPE; METABOLISM; METHODOLOGY; MOUSE MUTANT; TIME;

ANIMAL FEED; ANIMALS; CELL LINE; ELECTROPHYSIOLOGY; GENOTYPE; GLYCEROL; LIPIDS; MICE; MICE, KNOCKOUT; NERVE TISSUE; NEURAL CONDUCTION; PHOSPHOLIPID ETHERS; PHOSPHOLIPIDS; PLASMALOGENS; RECEPTORS, CYTOPLASMIC AND NUCLEAR; TIME FACTORS;

EID: 82755170548     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0028539     Document Type: Article

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