Expression and functional characterization of human mutant sulfamidase in insect cells

Molecular Genetics and Metabolism

Volumn 83, Issue 3, 2004, Pages 246-251

  Montfort, Magda ^a   Garrido, Elena ^a   Hopwood, John J ^b   Grinberg, Daniel ^a   Chabás, Amparo ^c   Vilageliu, Lluïsa ^a  

^a UNIVERSITY OF BARCELONA   (Spain)

^b Lysosomal Diseases Research Unit   (Australia)

^c Institut de Bioquimica Clinica Barcelona   (Spain)

Author keywords

Bac to bac baculovirus expression system; Heparan N sulfatase; Mucopolysaccharidosis IIIA; Sanfilippo syndrome; Sulfamidase; Transient expression

Indexed keywords

COMPLEMENTARY DNA;

ALLELE; ARTICLE; BACULOVIRUS; DNA POLYMORPHISM; ENZYME ACTIVITY; GENE EXPRESSION; GENE MUTATION; INSECT CELL; NONHUMAN; PRECURSOR; PRIORITY JOURNAL; WESTERN BLOTTING;

ALLELES; ANIMALS; BLOTTING, WESTERN; CELLS, CULTURED; DNA PRIMERS; DNA, COMPLEMENTARY; ELECTROPHORESIS, POLYACRYLAMIDE GEL; GENE EXPRESSION; GENOTYPE; HUMANS; HYDROLASES; MUCOPOLYSACCHARIDOSIS III; MUTAGENESIS, SITE-DIRECTED; MUTATION; SPAIN; SPODOPTERA;

INSECTA; UNIDENTIFIED BACULOVIRUS;

EID: 8144220016     PISSN: 10967192     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ymgme.2004.07.001     Document Type: Article

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