메뉴 건너뛰기




Volumn 365, Issue 18, 2011, Pages 1734-1735

Therapy for cystic fibrosis - The end of the beginning?

Author keywords

[No Author keywords available]

Indexed keywords

IVACAFTOR; TRANSMEMBRANE CONDUCTANCE REGULATOR;

EID: 80455144623     PISSN: 00284793     EISSN: 15334406     Source Type: Journal    
DOI: 10.1056/NEJMe1110323     Document Type: Editorial
Times cited : (27)

References (9)
  • 1
    • 80455162465 scopus 로고    scopus 로고
    • A CFTR potentiator in patients with cystic fibrosis and the G551D mutation
    • Ramsey BW, Davies J, McElvaney NG, et al. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. N Engl J Med 2011;365:1663-72.
    • (2011) N Engl J Med , vol.365 , pp. 1663-1672
    • Ramsey, B.W.1    Davies, J.2    McElvaney, N.G.3
  • 3
    • 78549279173 scopus 로고    scopus 로고
    • Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation
    • Accurso FJ, Rowe SM, Clancy JP, et al. Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation. N Engl J Med 2010;363:1991-2003.
    • (2010) N Engl J Med , vol.363 , pp. 1991-2003
    • Accurso, F.J.1    Rowe, S.M.2    Clancy, J.P.3
  • 4
    • 73249114731 scopus 로고    scopus 로고
    • Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770
    • Van Goor F, Hadida S, Grootenhuis PD, et al. Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770. Proc Natl Acad Sci U S A 2009;106:18825-30.
    • (2009) Proc Natl Acad Sci U S A , vol.106 , pp. 18825-18830
    • Van Goor, F.1    Hadida, S.2    Grootenhuis, P.D.3
  • 6
    • 77955607650 scopus 로고    scopus 로고
    • Peripheral protein quality control removes unfolded CFTR from the plasma membrane
    • Okiyoneda T, Barrière H, Bagdány M, et al. Peripheral protein quality control removes unfolded CFTR from the plasma membrane. Science 2010;329:805-10.
    • (2010) Science , vol.329 , pp. 805-810
    • Okiyoneda, T.1    Barrière, H.2    Bagdány, M.3
  • 8
    • 1542267080 scopus 로고    scopus 로고
    • State of the art: Why do the lungs of patients with cystic fibrosis become infected and why can't they clear the infection?
    • Chmiel JF, Davis PB. State of the art: why do the lungs of patients with cystic fibrosis become infected and why can't they clear the infection? Respir Res 2003;4:8.
    • (2003) Respir Res , vol.4 , pp. 8
    • Chmiel, J.F.1    Davis, P.B.2


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.