Left ventricular geometry, global function, and dyssynchrony in infants and children with pompe cardiomyopathy undergoing enzyme replacement therapy

Journal of Cardiac Failure

Volumn 17, Issue 11, 2011, Pages 930-936

  Chen, Chun An ^a   Chien, Yin Hsiu ^a   Hwu, Wuh Liang ^a   Lee, Ni Chung ^a   Wang, Jou Kou ^a   Chen, Lei Ru ^a   Lu, Chun Wei ^a   Lin, Ming Tai ^a   Chiu, Shuenn Nan ^a   Chiu, Hsin Hui ^a   Wu, Mei Hwan ^a  

^a NATIONAL TAIWAN UNIVERSITY HOSPITAL   (Taiwan)

Author keywords

dyssynchrony; enzyme replacement therapy; hypertrophic cardiomyopathy; Pompe disease

Indexed keywords

RECOMBINANT GLUCAN 1,4 ALPHA GLUCOSIDASE;

ARTICLE; CARDIOMYOPATHY; CLINICAL ARTICLE; CONTROLLED STUDY; ENZYME REPLACEMENT; FEMALE; GEOMETRY; HEART LEFT VENTRICLE; HEART LEFT VENTRICLE FUNCTION; HEART LEFT VENTRICLE HYPERTROPHY; HEART LEFT VENTRICLE MASS; HUMAN; INFANT; INFANTILE ONSET POMPE CARDIOMYOPATHY; MALE; MITRAL VALVE; MULTIVARIATE ANALYSIS; POMPE CARDIOMYOPATHY; PRIORITY JOURNAL; QRS COMPLEX; TISSUE DOPPLER IMAGING;

ADRENERGIC BETA-ANTAGONISTS; AGE FACTORS; ARRHYTHMIAS, CARDIAC; CARDIOMYOPATHY, HYPERTROPHIC; CASE-CONTROL STUDIES; CHILD, PRESCHOOL; DIASTOLE; DISEASE PROGRESSION; ENZYME REPLACEMENT THERAPY; FEMALE; GLYCOGEN STORAGE DISEASE TYPE II; HUMANS; HYPERTROPHY, LEFT VENTRICULAR; INFANT; INFANT, NEWBORN; MALE; MULTIVARIATE ANALYSIS; PROSPECTIVE STUDIES; STATISTICS, NONPARAMETRIC; SYSTOLE; TIME FACTORS; ULTRASONOGRAPHY, DOPPLER;

EID: 80255137080     PISSN: 10719164     EISSN: 15328414     Source Type: Journal    
DOI: 10.1016/j.cardfail.2011.07.011     Document Type: Article

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