ADAMTSL6β protein rescues fibrillin-1 microfibril disorder in a Marfan syndrome mouse model through the promotion of fibrillin-1 assembly

Journal of Biological Chemistry

Volumn 286, Issue 44, 2011, Pages 38602-38613

  Saito, Masahiro ^a   Kurokawa, Misaki ^a   Oda, Masahito ^a   Oshima, Masamitsu ^a   Tsutsui, Ko ^c   Kosaka, Kazutaka ^d   Nakao, Kazuhisa ^a   Ogawa, Miho ^a,b   Manabe, Ri Ichiroh ^g   Suda, Naoto ^f   Ganjargal, Ganburged ^f   Hada, Yasunobu ^a,f   Noguchi, Toshihide ^e   Teranaka, Toshio ^d   Sekiguchi, Kiyotoshi ^c   Yoneda, Toshiyuki ^c   Tsuji, Takashi ^a,b  

^a TOKYO UNIVERSITY OF SCIENCE   (Japan)

^b Organ Technologies Inc   (Japan)

^c OSAKA UNIVERSITY   (Japan)

^d KANAGAWA DENTAL COLLEGE   (Japan)

^e AICHI GAKUIN UNIVERSITY   (Japan)

^f TOKYO MEDICAL AND DENTAL UNIVERSITY   (Japan)

^g RIKEN YOKOHAMA INSTITUTE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

CONNECTIVE TISSUES; CURRENT DATA; EXTRACELLULAR MATRIX PROTEIN; FIBRILLIN-1; MARFAN SYNDROME; METALLO-PROTEASE; MICRO-FIBRILS; MICROFIBRIL; MICROFIBRIL ASSEMBLY; MOUSE MODELS; OCULAR LENS; PERIODONTAL DISEASE; PERIODONTAL LIGAMENT; THERAPEUTIC STRATEGY; THROMBOSPONDIN;

COLLAGEN; HISTOLOGY; MUSCULOSKELETAL SYSTEM; TISSUE;

MAMMALS;

ADAM PROTEIN; ADAMTSL6BETA PROTEIN; FIBRILLIN 1; TRANSFORMING GROWTH FACTOR BETA; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONNECTIVE TISSUE; CONTROLLED STUDY; DEVELOPMENT; FIBER; MARFAN SYNDROME; MOUSE; NONHUMAN; PERIODONTAL LIGAMENT; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN EXPRESSION; PROTEIN FUNCTION; TISSUE REGENERATION;

ANIMALS; DISEASE MODELS, ANIMAL; EXTRACELLULAR MATRIX; EXTRACELLULAR MATRIX PROTEINS; GENE EXPRESSION REGULATION, DEVELOPMENTAL; HUMANS; IMMUNOHISTOCHEMISTRY; MARFAN SYNDROME; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MICROFIBRILS; MICROFILAMENT PROTEINS; MODELS, GENETIC; RECOMBINANT PROTEINS; TOOTH; TRANSFORMING GROWTH FACTOR BETA; WOUND HEALING;

MUS;

EID: 80055086478     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M111.243451     Document Type: Article

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