rFVIIa administered by continuous infusion during surgery in patients with severe congenital FVII deficiency

Haemophilia

Volumn 17, Issue 5, 2011, Pages 764-770

  Tran, H T T ^a,b   Tjonnfjord G E ^b,c   Paus, A ^c   Holme, P A ^c  

^a OSLO UNIVERSITY HOSPITAL   (Norway)

^b UNIVERSITY OF OSLO   (Norway)

^c OSLO UNIVERSITY HOSPITAL   (Norway)

Author keywords

Congenital FVII deficiency; Cost; RFVIIa; Safety; Surgery

Indexed keywords

OCTAPLEX; PROTHROMBIN COMPLEX; RECOMBINANT BLOOD CLOTTING FACTOR 7A; TRANEXAMIC ACID; UNCLASSIFIED DRUG;

ADOLESCENT; ADULT; AGED; ARTICLE; BLEEDING; BLOOD CLOTTING FACTOR 7 DEFICIENCY; CLINICAL ARTICLE; CLINICAL TRIAL; CONTINUOUS INFUSION; CONTROLLED STUDY; COST EFFECTIVENESS ANALYSIS; DRUG COST; DRUG EFFICACY; DRUG SAFETY; FEMALE; HEMOSTASIS; HUMAN; MAJOR SURGERY; MALE; MINOR SURGERY; PERIOPERATIVE BLEEDING; PERIOPERATIVE COMPLICATION; PRIORITY JOURNAL; PROSPECTIVE STUDY; PROTHROMBIN TIME; THROMBIN TIME; TREATMENT DURATION;

ADOLESCENT; ADULT; BLOOD LOSS, SURGICAL; FACTOR VII DEFICIENCY; FACTOR VIIA; FEMALE; HEMOSTASIS, SURGICAL; HEMOSTATICS; HUMANS; INFUSIONS, INTRAVENOUS; MALE; MIDDLE AGED; PERIOPERATIVE CARE; PROSPECTIVE STUDIES; PROTHROMBIN TIME; RECOMBINANT PROTEINS; THROMBIN; TRANEXAMIC ACID; YOUNG ADULT;

EID: 80052033313     PISSN: 13518216     EISSN: 13652516     Source Type: Journal    
DOI: 10.1111/j.1365-2516.2011.02596.x     Document Type: Article

References (23)

1. Paula Bolton-Maggs and von Willebrand and rare bleeding disorders committee 2010-2012. What is factor VII deficiency? World Federation of Haemophilia, 2010.
2. Peyvandi F, Duga S, Akhavan S, Akhavan S, Mannucci MP. Rare coagulation deficiencies. Haemophilia 2002; 8: 308-21.
3. Ingerslev J, Kristensen HL. Clinical picture and treatment strategies in factor VII deficiency. Haemophilia 1998; 4: 689-96.
4. Mariani G, Dolce A, Marchetti G, Bernardi F. Clinical picture and management of congenital factor VII deficiency. Haemophilia 2004; 10: 180-3.
5. Triplett DA, Brandt JT, Batard MA, Dixon JL, Fair DS. Hereditary FVII deficiency: heterogenity defined by combined functional and immunochemical analysis. Blood 1985; 66: 1284-7.
6. Kelleher JF, Gomperts E, Davis W et al. Selection of replacement therapy for patients with severe FVII deficiency. Am J Pediatr Hematol Oncol 1986; 8: 318-23.
7. Lapecorella M, Mariani G. Factor VII deficiency: defining the clinical picture and optimizing therapeutic options. Haemophilia 2008; 14: 1170-5.
8. Niikura T, Nishikawa T, Saegusa Y, Fujishiro T, Yoshiya S, Kurosaka M. Total hip arthroplasty in severe congenital factor VII deficiency: successful use of recombinant activated factor VII for hemostasis. J Arthroplasty 2005; 20: 396-400.
9. Jimenez-Yuste V, Villar A, Morado M et al. Continuous infusion of recombinant activated factor VII during caesarean section delivery in a patient with congenital factor VII deficiency. Haemophilia 2000; 6: 588-90.
10. Schulman S, Tjønnfjord GE, Wallensten R, Martinowitz U, Kenet G. Continuous infusion of recombinant factor VIIa for surgery in patients with deficiency of factor VII. Thromb Haemost 2005; 94: 1177-80.
11. Brummel Ziedins K, Rivard GE, Pouliot RL et al. Factor VIIa replacement therapy in factor FVII deficiency. J Thromb Haemost 2004; 2: 1735-44.
12. Schulman S, Bech JM, Varon D et al. Feasibility of using recombinant factor VIIa in continuous infusion. Thromb Haemost 1996; 75: 432-6.
13. Schulman S. Safety, efficacy and lessons from continuous infusion with rFVIIa. Haemophilia 1998; 4: 564-7.
14. Mannucci PM, Duga S, Peyvandi F, Peyvandi F. Recessively inherited coagulation disorders. Blood 2004; 104: 1243-52.
15. Mathijssen NCJ, Masereeuw R, Holme PA et al. Pharmacokinetics of recombinant activated factor VII and plasma-derived factor VII in a cohort of severe FVII deficient patients. J Thromb Haemost. Submitted.
16. Mariani G, Dolce A, Batorova A et al. Recombinant, activated factor VII for surgery in factor VII deficiency: a prospective evaluation - the surgical STER. Br J Haematol 2011; 152: 340-6.
17. Cid AR, Lorenzo JI, Haya S, Montoro JM, Sasana P, Aznar JA. A comparison of FVII:C and FVIIa assay for the monitoring of recombinant FVIIa treatment. Haemophilia 2001; 7: 39-41.
18. Berntorp E, Salvagno L. Standardation and clinical utility of thrombin generation assays. Semin Thromb Hemost 2008; 34: 670-82.
19. Hemker HC, Giesen P, Aldieri R et al. The calibrated automated thrombogram (CAT): a universal routine test for hyper- and hypocoagulability. Pathophysiol Haemost Thromb 2002; 32: 249-53.
20. Barnett JM, Demel KC, Mega AE, Butera JN, Sweeney JD. Lack of bleeding in patients with severe factor VII deficiency. Am J Hematol 2005; 78: 134-7.
21. Godal HC, Madsen K, Nissen-Meyer R. Thrombo-embolism in patients with total proconvertin (Factor VII) deficiency. Acta Medica Scandinavia 1962; 171: 3-6.
22. Mariani G, Herrmann FH, Schulman S et al. Thrombosis in inherited factor VII deficiency. J Thromb Haemost 2003; 1: 2153-8.
23. Ingerslev J, Christiansen C, Sørensen B. Inhibitor to factor seven in severe factor VII deficiency: detection and course of the inhibitory response. J Thromb Haemost 2005; 3: 799-800.