Factor VII deficiency: Defining the clinical picture and optimizing therapeutic options

Haemophilia

Volumn 14, Issue 6, 2008, Pages 1170-1175

  Lapecorella, Mario ^a   Mariani, G ^a  

^a UNIVERSITY OF L'AQUILA   (Italy)

Author keywords

Clotting defect; FVII; FVII deficiency; Rare bleeding disorders; Replacement therapy; RFVIIa

Indexed keywords

BLOOD CLOTTING FACTOR 7; BLOOD CLOTTING FACTOR 7 CONCENTRATE; BLOOD CLOTTING FACTOR 8; BLOOD CLOTTING FACTOR CONCENTRATE; ENZYME PRECURSOR; FRESH FROZEN PLASMA; GENTAMICIN; PROTHROMBIN COMPLEX; PROVERTIN UM TIM3; RECOMBINANT BLOOD CLOTTING FACTOR 7A; THROMBOPLASTIN; TRANEXAMIC ACID; UNCLASSIFIED DRUG;

ARTICLE; BLEEDING; BLOOD CLOTTING FACTOR 7 DEFICIENCY; BRAIN HEMORRHAGE; CLINICAL FEATURE; CLINICAL TRIAL; CONTINUOUS INFUSION; COST EFFECTIVENESS ANALYSIS; DRUG BLOOD LEVEL; DRUG COST; DRUG EFFICACY; DRUG HALF LIFE; DRUG MECHANISM; DRUG SAFETY; FRAMESHIFT MUTATION; GASTROINTESTINAL HEMORRHAGE; GENETIC ANALYSIS; GENETIC POLYMORPHISM; HEMARTHROSIS; HUMAN; MOLECULAR GENETICS; PARTIAL THROMBOPLASTIN TIME; PATHOPHYSIOLOGY; PHENOTYPE; POLYMERASE CHAIN REACTION; PRENATAL DIAGNOSIS; PRIORITY JOURNAL; PROGNOSIS; THROMBOSIS;

AGE FACTORS; BLOOD COAGULATION; COAGULANTS; FACTOR VII; FACTOR VII DEFICIENCY; FACTOR VIIA; FEMALE; HEMORRHAGE; HUMANS; INFANT; INFANT, NEWBORN; MALE; MUTATION; PREGNANCY; PROTHROMBIN TIME; RANDOMIZED CONTROLLED TRIALS AS TOPIC; RARE DISEASES; RECOMBINANT PROTEINS; REGISTRIES; SEVERITY OF ILLNESS INDEX;

EID: 55949124238     PISSN: 13518216     EISSN: 13652516     Source Type: Journal    
DOI: 10.1111/j.1365-2516.2008.01844.x     Document Type: Article

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