Study of patients with Hyper-IgM type IV phenotype who recovered spontaneously during late childhood and review of the literature

European Journal of Pediatrics

Volumn 170, Issue 8, 2011, Pages 1039-1047

  Karaca, Neslihan Edeer ^a   Durandy, Anne ^b   Gulez, Nesrin ^a   Aksu, Guzide ^a   Kutukculer, Necil ^a  

^a EGE UNIVERSITY   (Turkey)

^b HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

Defective class switch recombination; Hyper IgM syndromes; Recovery with age

Indexed keywords

AMOXICILLIN; BACTERIUM LYSATE; CD40 ANTIGEN; CD40 LIGAND; IMMUNOGLOBULIN; IMMUNOGLOBULIN A; IMMUNOGLOBULIN E; IMMUNOGLOBULIN G; IMMUNOGLOBULIN G ANTIBODY; IMMUNOGLOBULIN G1; IMMUNOGLOBULIN G2; IMMUNOGLOBULIN G3; IMMUNOGLOBULIN G4; IMMUNOGLOBULIN M; TETANUS TOXOID;

ARTICLE; B LYMPHOCYTE; CD3+ T LYMPHOCYTE; CD4+ T LYMPHOCYTE; CD8+ T LYMPHOCYTE; CELL FUNCTION; CELL PROLIFERATION; CHILD; CLASS SWITCH RECOMBINATION; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; FOLLOW UP; GENE EXPRESSION; GENE MUTATION; HAEMOPHILUS INFLUENZAE TYPE B; HUMAN; HYPER IGM SYNDROME; HYPERIMMUNOGLOBULIN M TYPE IV; IMMUNOGLOBULIN BLOOD LEVEL; INFANT; INFECTION; LOWER RESPIRATORY TRACT INFECTION; LYMPHOCYTE COUNT; LYMPHOID HYPERPLASIA; MALE; MIXED INFECTION; PHENOTYPE; PRESCHOOL CHILD; PRIORITY JOURNAL; RECURRENT DISEASE; SOMATIC HYPERMUTATION; T LYMPHOCYTE; UPPER RESPIRATORY TRACT INFECTION; URINARY TRACT INFECTION;

B-LYMPHOCYTE SUBSETS; CHILD; CHILD, PRESCHOOL; FEMALE; FOLLOW-UP STUDIES; HUMANS; HYPER-IGM IMMUNODEFICIENCY SYNDROME; IMMUNOGLOBULINS; LYMPHOCYTE COUNT; MALE; PHENOTYPE; REMISSION, SPONTANEOUS; RETROSPECTIVE STUDIES;

EID: 79960948937     PISSN: 03406199     EISSN: 14321076     Source Type: Journal    
DOI: 10.1007/s00431-011-1400-2     Document Type: Article

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