Critical roles for the COOH terminus of the Cu-atpase ATP7B in protein stability, trans-Golgi network retention, copper sensing, and retrograde trafficking

American Journal of Physiology - Gastrointestinal and Liver Physiology

Volumn 301, Issue 1, 2011, Pages

  Braiterman, L ^a   Nyasae, L ^a   Leves, F ^a   Hubbard, A L ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Mutation; Wilson disease

Indexed keywords

COPPER; MENKES PROTEIN; WILSON DISEASE PROTEIN;

ARTICLE; CARBOXY TERMINAL SEQUENCE; DYNAMICS; FIBROBLAST; LIVER CELL; MUTATION; PHENOTYPE; PRIORITY JOURNAL; PROTEIN MOTIF; PROTEIN STABILITY; PROTEIN TRANSPORT; SENSITIVITY ANALYSIS; TRANS GOLGI NETWORK; WILSON DISEASE;

ADENOSINE TRIPHOSPHATASES; AMINO ACID SEQUENCE; CATION TRANSPORT PROTEINS; CELLS, CULTURED; COPPER; FIBROBLASTS; HEPATOCYTES; HEPATOLENTICULAR DEGENERATION; HUMANS; MOLECULAR SEQUENCE DATA; MUTATION; PROTEIN STABILITY; PROTEIN TRANSPORT; TRANS-GOLGI NETWORK;

EID: 79959851492     PISSN: 01931857     EISSN: 15221547     Source Type: Journal    
DOI: 10.1152/ajpgi.00038.2011     Document Type: Article

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