ALMS1-deficient fibroblasts over-express extra-cellular matrix components, display cell cycle delay and are resistant to apoptosis

PLoS ONE

Volumn 6, Issue 4, 2011, Pages

  Zulato, Elisabetta ^a   Favaretto, Francesca ^a   Veronese, Caterina ^a   Campanaro, Stefano ^a   Marshall, Jan D ^b   Romano, Sara ^a   Cabrelle, Anna ^a   Collin, Gayle B ^b   Zavan, Barbara ^a   Belloni, Anna S ^a   Rampazzo, Enrica ^a   Naggert, Jürgen K ^b   Abatangelo, Giovanni ^a   Sicolo, Nicola ^a   Maffei, Pietro ^a   Milan, Gabriella ^a   Vettor, Roberto ^a  

^a UNIVERSITY OF PADOVA   (Italy)

^b JACKSON LABORATORY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COLLAGEN; ALMS1 PROTEIN, HUMAN; MESSENGER RNA; PROTEIN;

ADULT; ALMS1 GENE; ALSTROM SYNDROME; APOPTOSIS; ARTICLE; CASE REPORT; CELL ACTIVITY; CELL CULTURE; CELL CYCLE; CELL CYCLE PARAMETERS; CELL CYCLE REGULATION; CELL MIGRATION; CELL MOTILITY; CELL VIABILITY; COLLAGEN SYNTHESIS; CONTROLLED STUDY; CYTOARCHITECTURE; EXTRACELLULAR MATRIX; FEMALE; FIBROBLAST; FIBROSIS; GENE; GENE EXPRESSION; GENE MUTATION; GENETIC ASSOCIATION; HUMAN; HUMAN CELL; HUMAN TISSUE; MALE; NUCLEOTIDE SEQUENCE; PHENOTYPE; PROTEIN EXPRESSION; ULTRASTRUCTURE; UPREGULATION; BIOLOGICAL MODEL; CELL SHAPE; CELL SIZE; DNA MICROARRAY; GENE EXPRESSION PROFILING; GENE EXPRESSION REGULATION; GENETICS; METABOLISM; PATHOLOGY;

ADULT; ALSTROM SYNDROME; APOPTOSIS; CELL CYCLE; CELL SHAPE; CELL SIZE; EXTRACELLULAR MATRIX; FEMALE; FIBROBLASTS; FIBROSIS; GENE EXPRESSION PROFILING; GENE EXPRESSION REGULATION; HUMANS; MALE; MODELS, BIOLOGICAL; OLIGONUCLEOTIDE ARRAY SEQUENCE ANALYSIS; PROTEINS; RNA, MESSENGER; YOUNG ADULT;

EID: 79955636919     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0019081     Document Type: Article

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