Identification of phosphorylated oligosaccharides in cells of patients with a congenital disorders of glycosylation (CDG-I)

Biochimie

Volumn 93, Issue 5, 2011, Pages 823-833

  Vleugels, Wendy ^a,b   Duvet, Sandrine ^b   Peanne, Romain ^b   Mir, Anne Marie ^b   Cacan, René ^b   Michalski, Jean Claude ^b   Matthijs, Gert ^a   Foulquier, François ^b  

^a UNIVERSITY OF LEUVEN   (Belgium)

^b UNIVERSITÉ DES SCIENCES ET TECHNOLOGIES DE LILLE   (France)

Author keywords

Congential disorders of glycosylation; Endoplasmic reticulum; N glycosylation

Indexed keywords

DOLICHOL; LIPOOLIGOSACCHARIDE; MANGANESE; OLIGOSACCHARIDE; PHOSPHORYLATED OLIGOSACCHARIDE; UNCLASSIFIED DRUG;

ARTICLE; CATABOLISM; CELL LABELING; CONCENTRATION (PARAMETERS); CONGENITAL DISORDER OF GLYCOSYLATION TYPE 1; CONTROLLED STUDY; ENZYME ACTIVITY; HUMAN; HUMAN TISSUE; HYDROLYSIS; MICROSOME MEMBRANE; PATHOPHYSIOLOGY; PROTEIN GLYCOSYLATION; SIGNAL TRANSDUCTION;

CELLS, CULTURED; CHROMATOGRAPHY, HIGH PRESSURE LIQUID; CONGENITAL DISORDERS OF GLYCOSYLATION; CYTOPLASM; ENDOPLASMIC RETICULUM; GLUCOSYLTRANSFERASES; HUMANS; MANNOSYLTRANSFERASES; MEMBRANE GLYCOPROTEINS; MICROSOMES; MUTATION, MISSENSE; OLIGOSACCHARIDES; PHOSPHORYLATION; PHOSPHOTRANSFERASES; PHOSPHOTRANSFERASES (PHOSPHOMUTASES); PYROPHOSPHATASES;

EID: 79953879681     PISSN: 03009084     EISSN: 61831638     Source Type: Journal    
DOI: 10.1016/j.biochi.2011.01.016     Document Type: Article

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