Dysregulated brain creatine kinase is associated with hearing impairment in mouse models of Huntington disease

Journal of Clinical Investigation

Volumn 121, Issue 4, 2011, Pages 1519-1523

  Lin, Yow Sien ^a,b   Chen, Chiung Mei ^c   Soong, Bing Wen ^a   Wu, Yih Ru ^c   Chen, Hui Mei ^b   Yeh, Wen Ying ^d   Wu, Dai Rong ^d   Lin, Yi Jun ^d   Poon, Paul Wai Fung ^e   Cheng, Mei Ling ^c   Wang, Chih Hung ^d,f   Chern, Yijuang ^a,b  

^a NATIONAL YANG MING UNIVERSITY   (Taiwan)

^b INSTITUTE OF BIOMEDICAL SCIENCES   (Taiwan)

^c CHANG GUNG UNIVERSITY   (Taiwan)

^d TRI SERVICE GENERAL HOSPITAL   (Taiwan)

^e NATIONAL CHENG KUNG UNIVERSITY   (Taiwan)

^f NATIONAL DEFENSE MEDICAL CENTER   (Taiwan)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE TRIPHOSPHATE; CREATINE; CREATINE KINASE BB; CREATINE PHOSPHATE;

ADULT; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CLINICAL ARTICLE; COCHLEA; CONTROLLED STUDY; EVOKED RESPONSE AUDIOMETRY; FEMALE; HEARING IMPAIRMENT; HUMAN; HUNTINGTON CHOREA; IMMUNOHISTOCHEMISTRY; MALE; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION;

ADULT; ANIMALS; AUDIOMETRY, PURE-TONE; BLOTTING, WESTERN; CASE-CONTROL STUDIES; COCHLEA; CREATINE; CREATINE KINASE, BB FORM; DISEASE MODELS, ANIMAL; EVOKED POTENTIALS, AUDITORY, BRAIN STEM; FEMALE; GENE EXPRESSION; HEARING LOSS; HUMANS; HUNTINGTON DISEASE; MALE; MICE; MICE, TRANSGENIC; MIDDLE AGED; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION;

EID: 79953322201     PISSN: 00219738     EISSN: 15588238     Source Type: Journal    
DOI: 10.1172/JCI43220     Document Type: Article

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