Trafficking abnormality and ER stress underlie functional deficiency of hearing impairmentassociated connexin-31 mutants

Protein and Cell

Volumn 1, Issue 10, 2010, Pages 935-943

  Xia, Kun ^a   Ma, Hong ^b   Xiong, Hui ^b   Pan, Qian ^a   Huang, Liangqun ^a   Wang, Danling ^a   Zhang, Zhuohua ^a,b  

^a CENTRAL SOUTH UNIVERSITY   (China)

^b BURNHAM INSTITUTE   (United States)

Author keywords

bip; gap junction; inner ear; protein folding

Indexed keywords

CONNEXIN 31; GLUCOSE REGULATED PROTEIN 78; LUCIFER YELLOW; MUTANT PROTEIN; TRITON X 100;

AMINO ACID SUBSTITUTION; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL CONTACT; CELL MIGRATION; CELLULAR DISTRIBUTION; CONTROLLED STUDY; ENDOPLASMIC RETICULUM STRESS; GAP JUNCTION; GENE DELETION; GENE MUTATION; GOLGI COMPLEX; HAIR CELL; HEARING IMPAIRMENT; INNER EAR; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN STABILITY; PROTEIN TRANSPORT; PROTEIN VARIANT; SPIRAL GANGLION; UPREGULATION; WILD TYPE;

EID: 79953151054     PISSN: 1674800X     EISSN: 16748018     Source Type: Journal    
DOI: 10.1007/s13238-010-0118-7     Document Type: Article

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