Prevention of large-vessel stenoses in atypical hemolytic uremic syndrome associated with complement dysregulation

Pediatric Nephrology

Volumn 26, Issue 1, 2011, Pages 155-157

  Davin, Jean Claude ^a   Majoie, Charles ^b   Groothoff, Jaap ^a   Gracchi, Valentina ^a   Bouts, Antonia ^a   Goodship, Timothy H J ^c   Loirat, Chantal ^d  

^a EMMA CHILDREN S HOSPITAL   (Netherlands)

^b ACADEMIC MEDICAL CENTER   (Netherlands)

^c NEWCASTLE UNIVERSITY   (United Kingdom)

^d HÔPITAL ROBERT DEBRÉ   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ECULIZUMAB; FRESH FROZEN PLASMA; COMPLEMENT;

BRAIN INFARCTION; BRONCHOSPASM; CASE REPORT; CHILD; COMPLEMENT DISORDER; DISEASE COURSE; FEMALE; GENE MUTATION; HEMOLYTIC UREMIC SYNDROME; HUMAN; HYPOTENSION; KIDNEY FUNCTION; KIDNEY TRANSPLANTATION; LETTER; MAGNETIC RESONANCE ANGIOGRAPHY; MONOZYGOTIC TWINS; OCCLUSIVE CEREBROVASCULAR DISEASE; PERITONEAL DIALYSIS; PLASMAPHERESIS; PRIORITY JOURNAL; REMISSION; TREATMENT OUTCOME; ADOLESCENT; ATYPICAL HEMOLYTIC UREMIC SYNDROME; BRAIN ATHEROSCLEROSIS; GENE EXPRESSION REGULATION; GENETICS; IMMUNOLOGY; MUTATION; PEDIGREE; PRESCHOOL CHILD; SIBLING;

ADOLESCENT; CHILD, PRESCHOOL; COMPLEMENT SYSTEM PROTEINS; FEMALE; GENE EXPRESSION REGULATION; HEMOLYTIC-UREMIC SYNDROME; HUMANS; INTRACRANIAL ARTERIOSCLEROSIS; MAGNETIC RESONANCE ANGIOGRAPHY; MUTATION; PEDIGREE; PLASMA EXCHANGE; SIBLINGS;

EID: 79953010396     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-010-1608-9     Document Type: Letter

References (6)

1. Davin JC, Strain L, Goodship TH (2008) Plasma therapy in atypical haemolytic uremic syndrome: lessons from a family with a factor H mutation. Pediatr Nephrol 23:1517-1521
2. Davin JC, Gracchi V, Bouts A, Groothoff JW, Strain L, Goodship T (2009) Maintenance of kidney function following treatment with eculizumab and discontinuation of plasma exchange after a third kidney transplant for atypical hemolytic uremic syndrome associated with a CFH mutation. Am J Kidney Dis 55:708-711
3. Vergouwen MD, Adriani KS, Roos YB, Groothoff JW, Majoie CB (2008) Proximal cerebral artery stenosis in a patient with haemolytic uremic syndrome. Am J Neuroradiol 29:e34 (Pubitemid 351684993)
4. Loirat C, Macher MA, Elmaleh-Berges M, Kwon T, Deschênes G, Goodship TH, Majoie C, Davin JC, Blanc R, Savatovsky J, Moret J, Fremeaux-Bacchi V (2010) Non-atheromatous arterial stenoses in atypical haemolytic uremic syndrome associated with complement dysregulation. Nephrol Dial Transplant. doi:10.1093/ndt/ gfq319
5. Wilson AC, Mitsnefes MM (2009) Cardiovascular disease in CKD in children: update on risk factors, risk assessment, and management. Am J Kidney Dis 54:345-360
6. Haskard DO, Boyle JJ, Mason JC (2008) The role of complement in atherosclerosis. Curr Opin Lipidol 19:478-482