Plasma therapy in atypical haemolytic uremic syndrome: Lessons from a family with a factor H mutation

Pediatric Nephrology

Volumn 23, Issue 9, 2008, Pages 1517-1521

  Davin, Jean Claude ^a   Strain, Lisa ^b   Goodship, Tim H J ^b  

^a EMMA CHILDREN S HOSPITAL   (Netherlands)

^b NEWCASTLE UNIVERSITY   (United Kingdom)

Author keywords

Atypical HUS; FH mutation; Kidney transplantation; Plasma exchange; Plasma infusion

Indexed keywords

ACICLOVIR; ANTIHISTAMINIC AGENT; AZATHIOPRINE; BASILIXIMAB; COMPLEMENT FACTOR H; CYCLOSPORIN A; GANCICLOVIR; IMMUNOSUPPRESSIVE AGENT; INTERLEUKIN 2 RECEPTOR ANTIBODY; MEMBRANE COFACTOR PROTEIN; METHYLPREDNISOLONE; MYCOPHENOLIC ACID 2 MORPHOLINOETHYL ESTER; PREDNISONE; STEROID; THYMOCYTE ANTIBODY;

ACUTE GRAFT REJECTION; ALLERGIC REACTION; ARTICLE; CASE REPORT; COMPLEMENT ACTIVATION; CYTOMEGALOVIRUS INFECTION; DRUG BLOOD LEVEL; FAMILY STUDY; FEMALE; GENE MUTATION; GENETIC RISK; GENOTYPE; HEMOLYTIC UREMIC SYNDROME; HETEROZYGOSITY; HUMAN; HUMAN TISSUE; KIDNEY BIOPSY; KIDNEY GRAFT REJECTION; KIDNEY TRANSPLANTATION; LOW DRUG DOSE; MONOZYGOTIC TWINS; MUTATIONAL ANALYSIS; OUTCOME ASSESSMENT; PLASMAPHERESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; SINGLE NUCLEOTIDE POLYMORPHISM; SYMPTOMATOLOGY;

CHILD, PRESCHOOL; COMPLEMENT FACTOR H; DISEASES IN TWINS; FEMALE; HEMOLYTIC-UREMIC SYNDROME; HUMANS; KIDNEY TRANSPLANTATION; MUTATION; PLASMA EXCHANGE;

EID: 47749148096     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-008-0833-y     Document Type: Article

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