Glycogen storage disease type Ia in canines: A model for human metabolic and genetic liver disease

Journal of Biomedicine and Biotechnology

Volumn 2011, Issue , 2011, Pages

  Conlon, Thomas J ^a,b   Specht, Andrew ^a   Fiske, Laurie ^b   Erger, Kirsten ^a   Cossette, Travis ^a   Verstegen, John ^a   Campbell Thompson, Martha ^b   Struck, Maggie B ^a   Lee, Young Mok ^c   Chou, Janice Y ^c   Byrne, Barry J ^a,b   Correia, Catherine E ^b   Mah, Cathryn S ^a,b   Weinstein, David A ^b  

^a UNIVERSITY OF FLORIDA   (United States)

^b UNIVERSITY OF FLORIDA COLLEGE OF MEDICINE   (United States)

^c EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BIOLOGICAL MARKER; GLUCOSE; GLUCOSE 6 PHOSPHATASE; GLUCOSE 6 PHOSPHATASE ALPHA; GLUCOSE 6 PHOSPHATE; GLYCOGEN; LACTIC ACID; PARVOVIRUS VECTOR; STARCH; UNCLASSIFIED DRUG;

CARBOHYDRATE DIET; CLINICAL FEATURE; DISEASE SIMULATION; DNA SEQUENCE; DOG; DRUG EFFECT; DRUG EFFICACY; DRUG MECHANISM; ENZYME ACTIVITY; FATTY LIVER; FETUS MORTALITY; GENETIC SCREENING; GLUCONEOGENESIS; GLYCOGEN STORAGE DISEASE TYPE 1; GLYCOGEN STORAGE DISEASE TYPE 1A; GLYCOGENOLYSIS; HEPATOMEGALY; HETEROZYGOTE DETECTION; HUMAN; HUMAN VERSUS ANIMAL COMPARISON; HYPERLACTATEMIA; HYPERLIPIDEMIA; HYPERURICEMIA; HYPOGLYCEMIA; LACTIC ACIDOSIS; LIFESPAN; LIVER DISEASE; NONHUMAN; NUTRITIONAL SUPPORT; PANCREATITIS; POLYMERASE CHAIN REACTION; REVIEW; RISK BENEFIT ANALYSIS; SEQUENCE HOMOLOGY; SITE DIRECTED MUTAGENESIS; SPECIES COMPARISON; VIRAL GENE DELIVERY SYSTEM; ANIMAL; ANIMAL DISEASE; CLINICAL TRIAL (TOPIC); DISEASE MODEL; DOG DISEASE; GENETICS; METABOLISM; PATHOLOGY;

ANIMALIA; CANIS FAMILIARIS; MURINAE;

ANIMALS; CLINICAL TRIALS AS TOPIC; DISEASE MODELS, ANIMAL; DOG DISEASES; DOGS; GLYCOGEN STORAGE DISEASE TYPE I; HUMANS; LIVER DISEASES;

EID: 79952217203     PISSN: 11107243     EISSN: 11107251     Source Type: Journal    
DOI: 10.1155/2011/646257     Document Type: Review

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