Homozygous mutation in SCN5A associated with atrial quiescence, recalcitrant arrhythmias, and poor capture thresholds

Heart Rhythm

Volumn 8, Issue 3, 2011, Pages 471-473

  Lopez, Keila N ^a   Decker, Jamie A ^a   Friedman, Richard A ^a   Kim, Jeffrey J ^a  

^a TEXAS CHILDREN S HOSPITAL   (United States)

Author keywords

Atrial standstill; Genetic basis of arrhythmias; Ion channelopathy; Pacing; Pediatric cardiology; Ventricular arrhythmias

Indexed keywords

ALANINE; AMIODARONE; SODIUM CHANNEL NAV1.5; THREONINE;

AMINO ACID SUBSTITUTION; ARTICLE; CARDIOVERSION; CASE REPORT; CHILD; DEFIBRILLATION; DEFIBRILLATOR; ELECTROCARDIOGRAM; EXTRACORPOREAL OXYGENATION; FEMALE; GENE MUTATION; GENETIC ANALYSIS; GENETIC ASSOCIATION; HEART ATRIUM PACING; HEART EJECTION FRACTION; HEART RHYTHM; HEART VENTRICLE FIBRILLATION; HEART VENTRICLE TACHYCARDIA; HOLTER MONITORING; HOMOZYGOSITY; HUMAN; PRESCHOOL CHILD; PRIORITY JOURNAL; QRS COMPLEX; QT INTERVAL; RESUSCITATION; SINUS BRADYCARDIA;

AMIODARONE; ANTI-ARRHYTHMIA AGENTS; ARRHYTHMIAS, CARDIAC; CARDIAC PACING, ARTIFICIAL; CARDIOPULMONARY RESUSCITATION; CHILD; DISEASES IN TWINS; ELECTROCARDIOGRAPHY; EXTRACORPOREAL MEMBRANE OXYGENATION; FEMALE; HEART ATRIA; HOMOZYGOTE; HUMANS; RECURRENCE; SODIUM CHANNELS; TACHYCARDIA, VENTRICULAR;

EID: 79952163943     PISSN: 15475271     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.hrthm.2010.10.014     Document Type: Article

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