Marginal level dystrophin expression improves clinical outcome in a strain of dystrophin/utrophin double knockout mice

PLoS ONE

Volumn 5, Issue 12, 2010, Pages

  Li, Dejia ^a   Yue, Yongping ^a   Duan, Dongsheng ^a  

^a University of Missouri   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

DYSTROPHIN; UTROPHIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DISEASE SEVERITY; DUCHENNE MUSCULAR DYSTROPHY; FEMALE; GENE EXPRESSION REGULATION; GENE SILENCING; GENOTYPE; HETEROZYGOSITY; KNOCKOUT MOUSE; MALE; MOUSE; MUSCLE CONTRACTILITY; MUSCLE FORCE; NONHUMAN; NULL ALLELE; OUTCOME ASSESSMENT; PHENOTYPE; POLYMERASE CHAIN REACTION; PROTEIN EXPRESSION; PROTEIN FUNCTION; SURVIVAL TIME; WEIGHT CHANGE; ANIMAL; BIOSYNTHESIS; BODY WEIGHT; C57BL MOUSE; FLUORESCENCE MICROSCOPY; GENETICS; HETEROZYGOTE; METHODOLOGY; MOUSE MUTANT; SPECIES DIFFERENCE;

MUS;

ANIMALS; BODY WEIGHT; DYSTROPHIN; FEMALE; GENE EXPRESSION REGULATION; HETEROZYGOTE; MALE; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MICROSCOPY, FLUORESCENCE; MUSCULAR DYSTROPHY, DUCHENNE; PHENOTYPE; SPECIES SPECIFICITY; UTROPHIN;

EID: 78650920451     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0015286     Document Type: Article

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