Hyperimmunoglobulinemia D and periodic fever syndrome in children. Review on therapy with biological drugs and case report

Acta Paediatrica, International Journal of Paediatrics

Volumn 100, Issue 1, 2011, Pages 21-25

  Korppi, M ^a   Van Gijn, M E ^b   Antila, K ^c  

^a TAMPERE UNIVERSITY OF TECHNOLOGY   (Finland)

^b UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^c NORTH KARELIA CENTRAL HOSPITAL   (Finland)

Author keywords

Anti inflammatory therapy; Fever; Hereditary diseases; Interleukin 1 = IL 1; Mevalonate kinase defiency

Indexed keywords

AZATHIOPRINE; C REACTIVE PROTEIN; CEFUROXIME; CLINDAMYCIN; COLCHICINE; CYTOTOXIC AGENT; ETANERCEPT; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE INHIBITOR; IMMUNOGLOBULIN; IMMUNOGLOBULIN D; INFLIXIMAB; INTERLEUKIN 1; INTERLEUKIN 1 RECEPTOR BLOCKING AGENT; INTERLEUKIN 6; PREDNISOLONE; RECOMBINANT INTERLEUKIN 1 RECEPTOR BLOCKING AGENT; SIMVASTATIN; STEROID; THALIDOMIDE; TUMOR NECROSIS FACTOR; TUMOR NECROSIS FACTOR ALPHA INHIBITOR;

ABDOMINAL PAIN; ADULT; ADULTHOOD; AUTOSOMAL RECESSIVE DISORDER; CASE REPORT; CERVICAL LYMPHADENOPATHY; CHILD; CLINICAL FEATURE; CYTOPENIA; DIARRHEA; DISEASE ASSOCIATION; DISEASE COURSE; FAMILIAL MEDITERRANEAN FEVER; FEMALE; FEVER; GENE MUTATION; HUMAN; HYPERIMMUNOGLOBULINEMIA D AND PERIODIC FEVER SYNDROME; IMMUNOGLOBULIN BLOOD LEVEL; IMMUNOGLOBULIN DEFICIENCY; INFANCY; INFANT; INFLAMMATORY DISEASE; KERATOPATHY; LEUKOCYTE; MALE; NEOPLASM; NUCLEOTIDE SEQUENCE; PATHOGENESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; RECURRENT FEVER; REVIEW; RHEUMATIC DISEASE; SCHOOL CHILD; SKIN MANIFESTATION; VOMITING;

ANTI-INFLAMMATORY AGENTS; FEMALE; FEVER; HUMANS; INFANT; INTERLEUKIN 1 RECEPTOR ANTAGONIST PROTEIN; MEVALONATE KINASE DEFICIENCY; PERIODICITY; SYNDROME; TREATMENT OUTCOME;

EID: 78650092436     PISSN: 08035253     EISSN: 16512227     Source Type: Journal    
DOI: 10.1111/j.1651-2227.2010.01974.x     Document Type: Review

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