B cell cytopenia in two brothers with hyper-IgD and periodic fever syndrome

European Journal of Pediatrics

Volumn 168, Issue 7, 2009, Pages 825-831

  Sornsakrin, M ^a   Wenner, K ^a   Ganschow, R ^a  

^a UNIVERSITY MEDICAL CENTER HAMBURG EPPENDORF   (Germany)

Author keywords

B cell cytopenia; Children; Complications; Hyper IgD syndrome; Treatment

Indexed keywords

ANTIBIOTIC AGENT; AZATHIOPRINE; CIMETIDINE; DEXAMETHASONE; IMMUNOGLOBULIN D; IMMUNOGLOBULIN G; MEVALONATE KINASE; PREDNISONE;

ABDOMINAL PAIN; ARTHRALGIA; ARTICLE; B CELL CYTOPENIA; BACTERIAL INFECTION; CASE REPORT; CERVICAL LYMPHADENOPATHY; CHILD; CHILL; CLINICAL ASSESSMENT; CLINICAL FEATURE; CYTOPENIA; DISEASE SEVERITY; DRUG DOSE INCREASE; DRUG DOSE REDUCTION; ENCEPHALITIS; FEVER; HEADACHE; HETEROZYGOSITY; HUMAN; HYPERIMMUNOGLOBULINEMIA D AND PERIODIC FEVER SYNDROME; IMMUNOGLOBULIN BLOOD LEVEL; IMMUNOGLOBULIN DEFICIENCY; INCIDENCE; MALE; MYCOPLASMA PNEUMONIA; PATHOGENESIS; PFAPA SYNDROME; PHARYNGITIS; PNEUMONIA; PRESCHOOL CHILD; PRIORITY JOURNAL; RECURRENT FEVER; SCHOOL CHILD; SINGLE DRUG DOSE; SOMNOLENCE; STOMATITIS; UPPER RESPIRATORY TRACT INFECTION; VOMITING;

AGAMMAGLOBULINEMIA; AZATHIOPRINE; B-LYMPHOCYTES; CHILD; FEVER; GLUCOCORTICOIDS; HETEROZYGOTE; HUMANS; IMMUNOGLOBULIN D; IMMUNOGLOBULINS, INTRAVENOUS; IMMUNOLOGIC FACTORS; IMMUNOSUPPRESSIVE AGENTS; INFANT; LYMPHOPENIA; MALE; MEVALONATE KINASE DEFICIENCY; MUTATION; PERIODICITY; PHOSPHOTRANSFERASES (ALCOHOL GROUP ACCEPTOR); PREDNISONE; SIBLINGS; SYNDROME;

EID: 67349138662     PISSN: 03406199     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00431-008-0843-6     Document Type: Article

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