Salicylate restores transport function and anion exchanger activity of missense pendrin mutations

Hearing Research

Volumn 270, Issue 1-2, 2010, Pages 110-118

  Ishihara, Kenji ^a,b   Okuyama, Shuhei ^a   Kumano, Shun ^a   Iida, Koji ^a   Hamana, Hiroshi ^a   Murakoshi, Michio ^a   Kobayashi, Toshimitsu ^c   Usami, Shinichi ^d   Ikeda, Katsuhisa ^e   Haga, Yoichi ^a   Tsumoto, Kohei ^f   Nakamura, Hiroyuki ^g   Hirasawa, Noriyasu ^a   Wada, Hiroshi ^a  

^a TOHOKU UNIVERSITY   (Japan)

^b IBARAKI UNIVERSITY   (Japan)

^c TOHOKU UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^d SHINSHU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^e JUNTENDO UNIVERSITY   (Japan)

^f UNIVERSITY OF TOKYO   (Japan)

^g Gakushuin University   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

MUTANT PROTEIN; PENDRIN; SALICYLIC ACID;

ANION EXCHANGE; ANION TRANSPORT; ARTICLE; CELL MEMBRANE; CELL STRAIN HEK293; CELLULAR DISTRIBUTION; CONTROLLED STUDY; CYTOPLASM; GENE; HUMAN; HUMAN CELL; JAPANESE; MISSENSE MUTATION; NUCLEOTIDE SEQUENCE; PDS GENE; PENDRED SYNDROME; PERCEPTION DEAFNESS; PRIORITY JOURNAL; PROTEIN LOCALIZATION;

ASIAN CONTINENTAL ANCESTRY GROUP; BIOLOGICAL TRANSPORT; CELL LINE; CELL MEMBRANE; CELL SURVIVAL; CYTOPLASM; HEARING LOSS, SENSORINEURAL; HUMANS; JAPAN; MEMBRANE TRANSPORT PROTEINS; MICROSCOPY, FLUORESCENCE; MUTATION, MISSENSE; PROTEIN TRANSPORT; SALICYLATES; TRANSFECTION;

EID: 78649812501     PISSN: 03785955     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.heares.2010.08.015     Document Type: Article

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