Long-term outcome of nephropathic cystinosis: A 20-year single-center experience

Pediatric Nephrology

Volumn 25, Issue 12, 2010, Pages 2459-2467

  Greco, Marcella ^a   Brugnara, Milena ^b   Zaffanello, Marco ^b   Taranta, Anna ^a   Pastore, Anna ^a   Emma, Francesco ^a  

^a BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

^b UNIVERSITY OF VERONA   (Italy)

Author keywords

Chronic renal failure; Cysteamine; Growth; Nephropathic cystinosis

Indexed keywords

INDOMETACIN; INSULIN; MERCAPTAMINE; PANCREAS ENZYME; RAMIPRIL; RECOMBINANT GROWTH HORMONE; THYROXINE;

ARTICLE; CHILD; CHRONIC KIDNEY FAILURE; CLINICAL ARTICLE; CTNS GENE; CYSTINOSIS; FEMALE; FOLLOW UP; GENE; GENE MUTATION; GROWTH CURVE; HUMAN; INFANT; KIDNEY FAILURE; KIDNEY FUNCTION; LONG TERM CARE; MALE; NEPHROPATHIC CYSTINOSIS; PRESCHOOL CHILD; PRIMARY TUMOR; PRIORITY JOURNAL; TREATMENT OUTCOME;

ADOLESCENT; ANGIOTENSIN-CONVERTING ENZYME INHIBITORS; CHILD; CHILD, PRESCHOOL; CYSTEAMINE; DISEASE PROGRESSION; DRUG THERAPY, COMBINATION; EARLY DIAGNOSIS; FEMALE; HUMANS; INFANT; ITALY; KAPLAN-MEIER ESTIMATE; KIDNEY; KIDNEY FAILURE, CHRONIC; LOGISTIC MODELS; MALE; NEPHROTIC SYNDROME; RETROSPECTIVE STUDIES; RISK ASSESSMENT; RISK FACTORS; TIME FACTORS; TREATMENT OUTCOME;

EID: 78449266465     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-010-1641-8     Document Type: Article

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