Semiautomated method for determination of cystine concentration in polymorphonuclear leukocytes

Clinical Chemistry

Volumn 46, Issue 4, 2000, Pages 574-576

  Pastore, Anna ^a   Lo Russo, Anna ^a   Greco, Marcella ^a   Rizzoni, Gianfranco ^a   Federici, Giorgio ^a  

^a Children's Hosp Res Inst B   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

CYSTINE;

AMINO ACID ANALYSIS; ARTICLE; AUTOMATION; CYSTINOSIS; HUMAN; LABORATORY DIAGNOSIS; NEUTROPHIL;

EID: 0034116512     PISSN: 00099147     EISSN: None     Source Type: Journal    
DOI: 10.1093/clinchem/46.4.560b     Document Type: Article

References (9)

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2. 2. Thoene JG, Oshima RG, Crawhall JC, Olson DL, Schneider JA. Cystinosis: intracellular cystine depletion by aminothiols in vitro and in vivo. J Clin Investig 1976;58:180-9.
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7. 7. Meister A, Larsson A. Glutathione synthetase deficiency and other disorders of the g-glutamyl cycle. In: Scriver CR, Beaudet AL, Sly WS, Valle D, eds. The metabolic bases of inherited disease, 7th ed. New York: McGraw-Hill, 1995:1461-73.
8. 8. Svardal AM, Mansoor MA, Ueland PM. Determination of reduced, oxidized and protein-bound glutathione in human plasma with precolumn derivatization with monobromobimane and liquid chromatography. Anal Biochem 1990;184:338-46.
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