Enzymatic pathways in the pathogenesis of hereditary angioedema: The role of C1 inhibitor therapy

Journal of Allergy and Clinical Immunology

Volumn 126, Issue 5, 2010, Pages 918-925

  Kaplan, Allen P ^a  

^a MEDICAL UNIVERSITY OF SOUTH CAROLINA   (United States)

Author keywords

Angioedema; Bradykinin; Endothelial cells; Factor XII; Kallikrein; Kininogen

Indexed keywords

BLOOD CLOTTING FACTOR 12; BLOOD CLOTTING FACTOR 12 FRAGMENT; BLOOD CLOTTING FACTOR 12A; BRADYKININ; BRADYKININ B2 RECEPTOR ANTAGONIST; CELL SURFACE RECEPTOR; COMPLEMENT COMPONENT C1Q; COMPLEMENT COMPONENT C1R; COMPLEMENT COMPONENT C1S INHIBITOR; COMPLEMENT COMPONENT C4; ECALLANTIDE; HEAT SHOCK PROTEIN 90; HIGH MOLECULAR WEIGHT KININOGEN; KALLIKREIN; KALLIKREIN INHIBITOR; MUTANT PROTEIN; PLASMIN; PROLINE CARBOXYPEPTIDASE; UNCLASSIFIED DRUG;

ANGIONEUROTIC EDEMA; CELL ACTIVATION; COMPLEMENT ACTIVATION; DISEASE SEVERITY; DRUG INDICATION; ENDOTHELIUM CELL; HUMAN; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN PROTEIN INTERACTION; RECEPTOR UPREGULATION; REVIEW; TREATMENT RESPONSE;

EID: 78049472226     PISSN: 00916749     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jaci.2010.08.012     Document Type: Article

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