Familial C4B deficiency and immune complex glomerulonephritis

Clinical Immunology

Volumn 137, Issue 1, 2010, Pages 166-175

  Soto, K ^a   Wu, Y L ^b   Ortiz, A ^c   Aparicio S R ^a   Yu, C Y ^b  

^a HOSPITAL FERNANDO FONSECA   (Portugal)

^b NATIONWIDE CHILDREN S HOSPITAL   (United States)

^c HOSPITAL UNIVERSITARIO FUNDACIÓN JIMÉNEZ DÍAZ   (Spain)

Author keywords

C4 allotyping and genotyping; Complement C4B deficiency; Copy number variation; Membranoproliferative glomerulonephritis

Indexed keywords

ALBUMIN; COMPLEMENT COMPONENT C3; COMPLEMENT COMPONENT C4; COMPLEMENT COMPONENT C4A; COMPLEMENT COMPONENT C4B; CREATININE; CYCLOPHOSPHAMIDE; DIPEPTIDYL CARBOXYPEPTIDASE INHIBITOR; HLA DQ ANTIGEN; HLA DR ANTIGEN; IMMUNOGLOBULIN G; METHYLPREDNISOLONE; MYCOPHENOLIC ACID; PREDNISOLONE;

ADULT; ALBUMIN BLOOD LEVEL; ANAPHYLACTOID PURPURA; ANASARCA; ARTICLE; CASE REPORT; COMPLEMENT COMPONENT C4B DEFICIENCY; COMPLEMENT DEFICIENCY; CREATININE URINE LEVEL; DRUG DOSE REDUCTION; ELECTRON MICROSCOPY; ENDOTHELIUM CELL; FAMILY; FAMILY HISTORY; FEMALE; FIBROSING ALVEOLITIS; GENE; GENOTYPE; HAPLOTYPE; HEMATURIA; HETEROZYGOSITY; HLA TYPING; HOMOZYGOSITY; HUMAN; HYPERTENSION; IMMUNE COMPLEX NEPHRITIS; IMMUNOGLOBULIN DEPOSITION; IMMUNOSUPPRESSIVE TREATMENT; KIDNEY BIOPSY; KIDNEY TUBULE DAMAGE; MEDICAL ABORTION; MEMBRANOPROLIFERATIVE GLOMERULONEPHRITIS; MULTIPLE CYCLE TREATMENT; NEPHROTIC SYNDROME; PATHOPHYSIOLOGY; PHENOTYPE; PODOCYTE; PREGNANCY; PRIORITY JOURNAL;

ADULT; COMPLEMENT C4A; COMPLEMENT C4B; CREATININE; FEMALE; GENOTYPE; GLOMERULONEPHRITIS, MEMBRANOPROLIFERATIVE; HAPLOTYPES; HETEROZYGOTE; HLA ANTIGENS; HOMOZYGOTE; HUMANS; KIDNEY; NEPHROTIC SYNDROME; PEDIGREE; POLYMORPHISM, RESTRICTION FRAGMENT LENGTH; PROTEINURIA; STEROID 21-HYDROXYLASE; TENASCIN;

EID: 77956617798     PISSN: 15216616     EISSN: 15217035     Source Type: Journal    
DOI: 10.1016/j.clim.2010.06.003     Document Type: Article

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