A modified lipid composition in Fabry disease leads to an intracellular block of the detergent-resistant membrane-associated dipeptidyl peptidase IV

Journal of Inherited Metabolic Disease

Volumn 33, Issue 4, 2010, Pages 445-449

  Maalouf, Katia ^a,c   Jia, Jia ^a   Rizk, Sandra ^b   Brogden, Graham ^a   Keiser, Markus ^a   Das, Anibh ^c   Naim, Hassan Y ^a  

^a UNIVERSITY OF VETERINARY MEDICINE HANNOVER   (Germany)

^b LEBANESE AMERICAN UNIVERSITY   (Lebanon)

^c HANNOVER MEDICAL SCHOOL   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA GALACTOSIDASE; DIPEPTIDYL PEPTIDASE IV; GLYCOLIPID; GLYCOSPHINGOLIPID; LYSOSOME ASSOCIATED MEMBRANE PROTEIN 2; MEMBRANE LIPID; MEMBRANE PROTEIN; MICROSOMAL AMINOPEPTIDASE; PHOSPHATIDYLETHANOLAMINE; TRITON X 100; DETERGENT; DPP4 PROTEIN, HUMAN; OCTOXINOL; PHOSPHATIDYLCHOLINE; SPHINGOLIPID;

ARTICLE; CELL MEMBRANE; CELL SURFACE; CHEMICAL COMPOSITION; CONTROLLED STUDY; ENZYME LOCALIZATION; FABRY DISEASE; FIBROBLAST; GENE CONTROL; HUMAN; HUMAN CELL; LIPID RAFT; LYSOSOME; PROTEIN EXPRESSION; PROTEIN LIPID INTERACTION; PROTEIN TRANSPORT; WILD TYPE; CULTURE TECHNIQUE; CYTOLOGY; DRUG EFFECTS; ENZYMOLOGY; GENETICS; GOLGI COMPLEX; INTRACELLULAR MEMBRANE; METABOLISM; PHYSIOLOGY;

ALPHA-GALACTOSIDASE; ANTIGENS, CD26; CELL CULTURE TECHNIQUES; DETERGENTS; FABRY DISEASE; FIBROBLASTS; GOLGI APPARATUS; HUMANS; INTRACELLULAR MEMBRANES; MEMBRANE PROTEINS; OCTOXYNOL; PHOSPHATIDYLCHOLINES; PHOSPHATIDYLETHANOLAMINES; PROTEIN TRANSPORT; SPHINGOLIPIDS; DIPEPTIDYL PEPTIDASE 4;

EID: 77956056607     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-010-9114-6     Document Type: Article

References (10)

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