A congenital activating mutant of WASp causes altered plasma membrane topography and adhesion under flow in lymphocytes

Blood

Volumn 115, Issue 26, 2010, Pages 5355-5365

  Burns, Siobhan O ^a,b   Killock, David J ^c   Moulding, Dale A ^a   Metelo, Joao ^a   Nunes, Joao ^a   Taylor, Ruth R ^d   Forge, Andrew ^d   Thrasher, Adrian J ^a,b   Ivetic, Aleksandar ^c  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

^b GREAT ORMOND STREET HOSPITAL   (United Kingdom)

^c KING'S COLLEGE LONDON   (United Kingdom)

^d UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

F ACTIN; L SELECTIN; THREONINE; WISKOTT ALDRICH SYNDROME PROTEIN; ACTIN;

ANIMAL CELL; ARTICLE; CELL ADHESION; CELL ISOLATION; CONTROLLED STUDY; CYTOARCHITECTURE; CYTOSKELETON; GENE MUTATION; HEMATOPOIESIS; HUMAN; LYMPHOCYTE FUNCTION; MICROVILLUS; MOUSE; MUTANT; NONHUMAN; NORMAL HUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN INTERACTION; PROTEIN LOCALIZATION; SCANNING ELECTRON MICROSCOPY; CELL CULTURE; CELL MEMBRANE; CYTOLOGY; GENE EXPRESSION; GENETICS; LEUKOPENIA; LYMPHOCYTE; METABOLISM; MONONUCLEAR CELL; MUTATION; TUMOR CELL LINE; ULTRASTRUCTURE; X CHROMOSOME LINKED DISORDER;

ACTINS; CELL ADHESION; CELL LINE, TUMOR; CELL MEMBRANE; CELLS, CULTURED; GENE EXPRESSION; GENETIC DISEASES, X-LINKED; HUMANS; L-SELECTIN; LEUKOCYTES, MONONUCLEAR; LEUKOPENIA; LYMPHOCYTES; MICROVILLI; MUTATION; WISKOTT-ALDRICH SYNDROME PROTEIN;

EID: 77955855361     PISSN: 00064971     EISSN: 15280020     Source Type: Journal    
DOI: 10.1182/blood-2009-08-236174     Document Type: Article

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