IgG4-positive multi-organ lymphoproliferative syndrome manifesting as chronic symmetrical sclerosing dacryo-sialadenitis with subsequent secondary portal hypertension and remarkable IgG4-linked IL-4 elevation

Rheumatology

Volumn 49, Issue 9, 2010, Pages 1789-1791

  Suzuki, Katsuya ^a   Tamaru, Jun Ichi ^a   Okuyama, Ayumi ^a   Kameda, Hideto ^a   Amano, Koichi ^a   Nagasawa, Hayato ^a   Nishi, Eiko ^a   Yoshimoto, Keiko ^a   Setoyama, Yumiko ^a   Kaneko, Keiko ^a   Osada, Hisato ^b   Honda, Norinari ^b   Sasaki, Yasutsuna ^c   Itoyama, Shinji ^a   Tsuzaka, Kensei ^a   Takeuchi, Tsutomu ^a,d  

^a SAITAMA MEDICAL UNIVERSITY   (Japan)

^b SAITAMA MEDICAL UNIVERSITY   (Japan)

^c SAITAMA MEDICAL UNIVERSITY INTERNATIONAL MEDICAL CENTER   (Japan)

^d KEIO UNIVERSITY   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

IMMUNOGLOBULIN G4; INTERLEUKIN 4; METHYLPREDNISOLONE; PREDNISOLONE;

ABDOMINAL DISTENSION; ABDOMINAL RADIOGRAPHY; ADULT; AUTOIMMUNE PANCREATITIS; CASE REPORT; CLINICAL FEATURE; FEMALE; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; LETTER; LYMPHOPROLIFERATIVE DISEASE; MIKULICZ DISEASE; PLASMA CELL GRANULOMA; PORTAL HYPERTENSION; PRIORITY JOURNAL; SALIVARY GLAND BIOPSY; SCLEROSING DACRYOSIALOADENITIS; SIALOADENITIS; SYSTEMIC SCLEROSIS;

ADRENAL CORTEX HORMONES; AUTOIMMUNE DISEASES; CHRONIC DISEASE; DIAGNOSIS, DIFFERENTIAL; FEMALE; HUMANS; HYPERTENSION; IMMUNOGLOBULIN G; MIDDLE AGED; SCLEROSIS; SIALADENITIS; SYNDROME; TIME FACTORS; TREATMENT OUTCOME;

EID: 77955738272     PISSN: 14620324     EISSN: 14620332     Source Type: Journal    
DOI: 10.1093/rheumatology/keq113     Document Type: Letter

References (10)

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