Abnormal interaction of motor neuropathy-associated mutant HspB8 (Hsp22) forms with the RNA helicase Ddx20 (gemin3)

Cell Stress and Chaperones

Volumn 15, Issue 5, 2010, Pages 567-582

  Sun, Xiankui ^a   Fontaine, Jean Marc ^a   Hoppe, Adam D ^a   Carra, Serena ^b,f   Deguzman, Cheryl ^a   Martin, Jody L ^c   Simon, Stephanie ^d   Vicart, Patrick ^d   Welsh, Michael J ^a   Landry, Jacques ^b   Benndorf, Rainer ^a,e,g  

^a UNIVERSITY OF MICHIGAN MEDICAL SCHOOL   (United States)

^b LAVAL UNIVERSITY   (Canada)

^c LOYOLA UNIVERSITY MEDICAL CENTER   (United States)

^d Groupe Hospitalier Pitié Salpêtrière   (France)

^e OHIO STATE UNIVERSITY   (United States)

^f UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

^g THE RESEARCH INSTITUTE AT NATIONWIDE CHILDREN S HOSPITAL   (United States)

Author keywords

Charcot Marie Tooth disease; Ddx20; Heat shock protein B8; Motor neuropathy; Protein protein interaction; Survival of motor neurons protein

Indexed keywords

DEAD BOX PROTEIN 20; HEAT SHOCK PROTEIN 22; HEAT SHOCK PROTEIN 27; SURVIVAL MOTOR NEURON PROTEIN; SURVIVAL MOTOR NEURON PROTEIN 1;

ARTICLE; CONTROLLED STUDY; FLUORESCENCE RESONANCE ENERGY TRANSFER; GENE MUTATION; GENETIC ASSOCIATION; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOPRECIPITATION; INFANT MORTALITY; ISOELECTRIC POINT; MOTOR NEURON DISEASE; NUCLEOTIDE SEQUENCE; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN BINDING; PROTEIN CROSS LINKING; PROTEIN PROTEIN INTERACTION; SIGNAL TRANSDUCTION; SITE DIRECTED MUTAGENESIS; SPINAL MUSCULAR ATROPHY;

EID: 77955711004     PISSN: 13558145     EISSN: 14661268     Source Type: Journal    
DOI: 10.1007/s12192-010-0169-y     Document Type: Article

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